{"id":"W2115926629","doi":"10.1186/1710-1492-9-29","title":"Hereditary angioedema with C1 inhibitor deficiency: delay in diagnosis in Europe","year":2013,"lang":"en","type":"article","venue":"Allergy Asthma and Clinical Immunology","topic":"Coagulation, Bradykinin, Polyphosphates, and Angioedema","field":"Medicine","cited_by":149,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Hereditary angioedema; Icatibant; Medicine; Angioedema; C1-inhibitor; Disease; Laryngeal Edema; Observational study; Pediatrics; Family history; Dermatology; Surgery; Intensive care medicine; Edema; Internal medicine","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003206105,0.0002401613,0.0006038762,0.0001831333,0.00006013297,0.00002057563,0.0001288701,0.0003223758,0.0004809925],"category_scores_gemma":[0.0003198,0.0001887036,0.00009150444,0.0004949191,0.0004382722,0.0001883721,0.0001151316,0.0004223398,0.0001358327],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00002744033,"about_ca_system_score_gemma":0.0001319595,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001643052,"about_ca_topic_score_gemma":0.002654133,"domain_scores_codex":[0.997814,0.0001904402,0.0008365141,0.0005298676,0.0001455587,0.0004836142],"domain_scores_gemma":[0.9987034,0.0005714733,0.0001289673,0.0003185383,0.0001329767,0.0001446904],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0004939629,0.001127166,0.9314879,0.00001691526,0.0001722509,0.0004458306,0.0003491868,0.00001210808,0.00009600597,0.001033364,0.001804902,0.06296045],"study_design_scores_gemma":[0.003573552,0.001755613,0.9820825,0.0001629007,0.00001664447,0.0001890551,0.000289876,0.0002333415,0.00005719139,0.0002772741,0.01113623,0.0002258203],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9858913,0.008206793,0.00001834746,0.003933304,0.0003120035,0.0003427363,0.000001827432,0.00004922801,0.001244465],"genre_scores_gemma":[0.99468,0.003081397,0.0003774556,0.001086009,0.0001839463,0.00008910554,0.00002885196,0.00003254649,0.0004406256],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.06273463,"threshold_uncertainty_score":0.7695111,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01516617319128132,"score_gpt":0.27196444340361,"score_spread":0.2567982702123287,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}