{"id":"W2115926629","doi":"10.1186/1710-1492-9-29","title":"Hereditary angioedema with C1 inhibitor deficiency: delay in diagnosis in Europe","year":2013,"lang":"en","type":"article","venue":"Allergy Asthma and Clinical Immunology","topic":"Coagulation, Bradykinin, Polyphosphates, and Angioedema","field":"Medicine","cited_by":149,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Hereditary angioedema; Icatibant; Medicine; Angioedema; C1-inhibitor; Disease; Laryngeal Edema; Observational study; Pediatrics; Family history; Dermatology; Surgery; Intensive care medicine; Edema; Internal medicine","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001238333,0.0001532456,0.0002431999,0.0005627619,0.000187622,0.0005877959,0.0002082313,0.0003225383,0.001781585],"category_scores_gemma":[0.003815881,0.00006057505,0.0001652818,0.001240006,0.0002375637,0.0004420438,0.000394951,0.0002945129,0.0001307662],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004652111,"about_ca_system_score_gemma":0.0005856476,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.004730102,"about_ca_topic_score_gemma":0.001943727,"domain_scores_codex":[0.9993501,0.0001694945,0.00009761646,0.00016933,0.00009786459,0.0001156225],"domain_scores_gemma":[0.9968393,0.001007565,0.001482012,0.00007800066,0.0002403279,0.0003529224],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0003189332,0.00005080928,0.9747864,0.0001062201,0.00005857528,0.001299927,0.0002571538,0.000351075,0.0004713383,0.0004243218,0.0007642824,0.02111099],"study_design_scores_gemma":[0.00004336885,0.000243143,0.9810002,0.0002916684,0.00007400712,0.009791032,0.0009988657,0.0004590978,0.0005354533,0.0004465529,0.006103099,0.00001365696],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.989816,0.006282793,0.0004372561,0.0003740941,0.0000390542,0.00001110441,0.0005306226,0.00001117422,0.002497907],"genre_scores_gemma":[0.9981342,0.001290917,0.000167436,0.00007713018,0.00001513136,0.000003756575,0.0002003721,0.000002114224,0.0001089946],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.004730102,"threshold_uncertainty_score":0.009405136,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01516617319128132,"score_gpt":0.27196444340361,"score_spread":0.2567982702123287,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}