{"id":"W2119182840","doi":"10.1177/1073858410386236","title":"Gene Therapy in Mouse Models of Huntington Disease","year":2011,"lang":"en","type":"review","venue":"The Neuroscientist","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":20,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of British Columbia","funders":"National Institute of Neurological Disorders and Stroke; Hereditary Disease Foundation","keywords":"Neuropathology; Huntingtin; Huntington's disease; Disease; Neuroscience; Huntingtin Protein; Biology; Gene knockin; Psychology; Bioinformatics; Medicine; Gene; Genetics; Pathology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004530611,0.0009125533,0.001129399,0.001359789,0.0001815425,0.0005214693,0.0007052735,0.001119974,0.00209665],"category_scores_gemma":[0.0002285631,0.0001918104,0.000373856,0.0008685489,0.0003807162,0.0006025143,0.0003790792,0.001301262,0.002659349],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004146992,"about_ca_system_score_gemma":0.0003253397,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0004696435,"about_ca_topic_score_gemma":0.0008670969,"domain_scores_codex":[0.9998732,0.00002328185,0.00001554136,0.00002445093,0.00005406105,0.000009499222],"domain_scores_gemma":[0.9999256,0.00002911506,0.0000145204,0.000004760592,0.0000169586,0.000008985676],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0001354467,0.0002136592,0.0001494116,0.0104056,0.000103077,0.0008441868,0.00007674037,0.0005137636,0.04214402,0.00599526,0.02683083,0.9125879],"study_design_scores_gemma":[0.00006906161,0.0003141,0.0008681793,0.001679179,0.0001173897,0.003697021,0.00003062528,0.0001360661,0.01046852,0.002327245,0.9802596,0.00003310087],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.0009225711,0.9930595,0.001331209,0.0002721269,0.0002953372,0.00002937035,0.00005164364,0.0000567564,0.00398147],"genre_scores_gemma":[0.003191153,0.9920511,0.001344117,0.0003229119,0.0001357215,0.00004528946,0.0001119129,0.000009753074,0.002788035],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.00209665,"threshold_uncertainty_score":0.007013977,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.1397249982109157,"score_gpt":0.3287872058894811,"score_spread":0.1890622076785654,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}