{"id":"W2120280549","doi":"10.2215/cjn.08091109","title":"Assessment of Renal Pathology and Dysfunction in Children with Fabry Disease","year":2010,"lang":"en","type":"review","venue":"Clinical Journal of the American Society of Nephrology","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":45,"is_retracted":false,"has_abstract":true,"ca_institutions":"Université de Montréal","funders":"National Institute of Neurological Disorders and Stroke","keywords":"Medicine; Fabry disease; Albuminuria; Proteinuria; Renal pathology; Disease; Enzyme replacement therapy; Renal biopsy; Renal function; Kidney; Internal medicine; Pathology; Biopsy; Pediatrics; Urology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0007849734,0.0007145192,0.001765313,0.0028762,0.0001493474,0.00060899,0.0006355179,0.0007168197,0.0008539806],"category_scores_gemma":[0.0009810667,0.0002098561,0.0003486417,0.001860379,0.0004046193,0.0008773303,0.0004239435,0.0008038128,0.000735241],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003808834,"about_ca_system_score_gemma":0.0007037836,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001407455,"about_ca_topic_score_gemma":0.002003122,"domain_scores_codex":[0.999757,0.00005710911,0.00004883767,0.00003797755,0.00008513405,0.00001395775],"domain_scores_gemma":[0.9995564,0.0002056071,0.00008071942,0.00001050364,0.000119061,0.00002781131],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00008491566,0.00005315169,0.00346248,0.01073285,0.0001192617,0.0009468434,0.0001013704,0.000174658,0.00118701,0.0007397966,0.01086486,0.9715328],"study_design_scores_gemma":[0.0000778218,0.0003572693,0.04814525,0.02340432,0.0007963239,0.04326329,0.0007055328,0.0003920532,0.002161619,0.002949029,0.8776452,0.0001023089],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.0003928505,0.9986808,0.0001319027,0.0001427433,0.00004521813,0.00000337018,0.00001421642,0.000005436988,0.000583531],"genre_scores_gemma":[0.002116743,0.9971252,0.0003659804,0.00008631086,0.00007846718,0.000005725818,0.00002562932,8.79395e-7,0.0001950497],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.0028762,"threshold_uncertainty_score":0.004151404,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04768597266141075,"score_gpt":0.4220950967453886,"score_spread":0.3744091240839779,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}