{"id":"W2121496322","doi":"10.1183/09031936.00104712","title":"Clinical phenotypes of Italian and Spanish patients with α<sub>1</sub>-antitrypsin deficiency","year":2012,"lang":"en","type":"article","venue":"European Respiratory Journal","topic":"Protease and Inhibitor Mechanisms","field":"Biochemistry, Genetics and Molecular Biology","cited_by":72,"is_retracted":false,"has_abstract":true,"ca_institutions":"University Hospital Foundation","funders":"Grifols; Fondazione IRCCS Policlinico San Matteo","keywords":"Medicine; Chronic bronchitis; Bronchitis; Internal medicine; Asthma; Lung function; COPD; Alpha 1-antitrypsin deficiency; Pediatrics; Respiratory system; Respiratory disease; Lung","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00121704,0.0003741149,0.0004553684,0.001069588,0.0002802991,0.0004978694,0.0002550714,0.0003332387,0.001211989],"category_scores_gemma":[0.00274298,0.0001894477,0.0003262491,0.001250133,0.0002709902,0.0001719051,0.0004945592,0.0002071711,0.0003004172],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005410165,"about_ca_system_score_gemma":0.0004251403,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0147057,"about_ca_topic_score_gemma":0.009087184,"domain_scores_codex":[0.9994552,0.0001778777,0.00007762791,0.0001212723,0.00006578144,0.0001022553],"domain_scores_gemma":[0.99872,0.0002561955,0.0005716357,0.0001291595,0.0001639972,0.0001591104],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.000187882,0.00001794357,0.9975625,0.000008782715,0.00002286021,0.0001814183,0.0001327054,0.0000452669,0.0001652475,0.00001968748,0.0002181496,0.001437594],"study_design_scores_gemma":[0.00002245861,0.00005730359,0.9986333,0.000006776653,0.00001359137,0.0006279794,0.0001714758,0.00008146937,0.00002603893,0.00001641226,0.0003405321,0.000002722024],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.998661,0.0001779794,0.00005339964,0.00003362728,0.000003180776,0.00001163118,0.0005031581,0.000003466498,0.0005524715],"genre_scores_gemma":[0.9976798,0.0001900088,0.0001379386,0.00005125017,0.00001300899,0.00002307489,0.001723358,0.000004142051,0.0001776004],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.0147057,"threshold_uncertainty_score":0.02924019,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0148001323750512,"score_gpt":0.2431042331687881,"score_spread":0.2283041007937369,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}