{"id":"W2121580159","doi":"10.1002/mds.10708","title":"Dystonia as a presenting sign of spinocerebellar ataxia type 1","year":2004,"lang":"en","type":"article","venue":"Movement Disorders","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":32,"is_retracted":false,"has_abstract":true,"ca_institutions":"Toronto Western Hospital; University of Toronto; University Health Network","funders":"","keywords":"Blepharospasm; Dystonia; Ataxia; Spinocerebellar ataxia; Medicine; Physical medicine and rehabilitation; Cerebellar ataxia; Neurological disorder; Pediatrics; Sign (mathematics); Focal dystonia; Psychology; Physical therapy; Central nervous system disease; Surgery; Psychiatry","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00005422676,0.0001636612,0.0001421702,0.00007669481,0.0001081437,0.00002710349,0.000280944,0.00002772673,0.0002188363],"category_scores_gemma":[0.0003254406,0.0001623252,0.00007284784,0.0003292036,0.0001241324,0.00007742664,0.0001193472,0.00006588195,0.0001100863],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00003253155,"about_ca_system_score_gemma":0.00009300985,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0001776016,"about_ca_topic_score_gemma":0.00004076744,"domain_scores_codex":[0.9985801,0.00006766873,0.0002374202,0.0004203417,0.0003974672,0.0002969856],"domain_scores_gemma":[0.9993865,0.00003804794,0.0001167188,0.0003367112,0.00003949289,0.00008251042],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.00003121912,0.000368378,0.009050145,0.000042243,0.00001063215,0.000006971027,0.0003021079,0.006203637,0.977533,0.005199867,0.000707357,0.0005444408],"study_design_scores_gemma":[0.000640465,0.0002016223,0.007468708,0.00001422081,0.00001498066,1.584864e-7,0.0001174911,0.00006453903,0.9582817,0.0324664,0.0005618012,0.0001679222],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9936951,0.00009909509,0.0002686188,0.0006569447,0.0001966111,0.0004179551,0.00001256281,0.00004816965,0.004604882],"genre_scores_gemma":[0.996508,0.00007461319,0.0001738527,0.002537869,0.00001918135,0.00001850403,0.000003075662,0.00002570213,0.000639225],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.02726654,"threshold_uncertainty_score":0.6619428,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01976639147489576,"score_gpt":0.2648698468247832,"score_spread":0.2451034553498875,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}