{"id":"W2121580159","doi":"10.1002/mds.10708","title":"Dystonia as a presenting sign of spinocerebellar ataxia type 1","year":2004,"lang":"en","type":"article","venue":"Movement Disorders","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":32,"is_retracted":false,"has_abstract":true,"ca_institutions":"Toronto Western Hospital; University of Toronto; University Health Network","funders":"","keywords":"Blepharospasm; Dystonia; Ataxia; Spinocerebellar ataxia; Medicine; Physical medicine and rehabilitation; Cerebellar ataxia; Neurological disorder; Pediatrics; Sign (mathematics); Focal dystonia; Psychology; Physical therapy; Central nervous system disease; Surgery; Psychiatry","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001780771,0.001185479,0.0007162897,0.0009821455,0.0007643733,0.0006314104,0.0004364286,0.001815449,0.001371655],"category_scores_gemma":[0.001655157,0.0004076636,0.0003710618,0.0005805246,0.0006205459,0.0007747831,0.000587073,0.000946447,0.00062242],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000428867,"about_ca_system_score_gemma":0.0003381423,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002577067,"about_ca_topic_score_gemma":0.003315703,"domain_scores_codex":[0.9997829,0.00003065154,0.00002226755,0.00004384897,0.00002816893,0.0000922657],"domain_scores_gemma":[0.9995041,0.0001251449,0.0001417842,0.00003345499,0.00003377937,0.0001616882],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.00009552939,0.00002771173,0.02932847,0.00004646877,0.00001357883,0.9625406,0.0002757455,0.00008195826,0.004433547,0.0001055857,0.000345652,0.002705064],"study_design_scores_gemma":[0.00002082588,0.0002578749,0.04126982,0.00002191993,0.00003612404,0.9565436,0.0001293929,0.0002219191,0.0007657275,0.00009985254,0.0006116144,0.00002134019],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9870968,0.003588949,0.0008778494,0.0007130871,0.0001296811,0.00006964253,0.0001679449,0.0001300038,0.007226194],"genre_scores_gemma":[0.9977512,0.001048957,0.0002558284,0.0002320526,0.0001823331,0.000006986943,0.00007066556,0.000007648428,0.000444361],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002577067,"threshold_uncertainty_score":0.005124152,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01976639147489576,"score_gpt":0.2648698468247832,"score_spread":0.2451034553498875,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}