{"id":"W2125180155","doi":"10.1056/nejmoa1309199","title":"Deficiency of Innate and Acquired Immunity Caused by an <i>IKBKB</i> Mutation","year":2013,"lang":"en","type":"article","venue":"New England Journal of Medicine","topic":"NF-κB Signaling Pathways","field":"Biochemistry, Genetics and Molecular Biology","cited_by":185,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of Saskatchewan","funders":"European Society for Immunodeficiencies; Bundesministerium für Bildung und Forschung","keywords":"Immunology; Immune system; Acquired immune system; Innate immune system; Biology; Immunity; Immunodeficiency; Medicine; Hypogammaglobulinemia; T cell; Genetics; Antibody","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001810485,0.0009193023,0.0002836674,0.0005483669,0.0003759958,0.0002056142,0.0002222069,0.0003929312,0.003208663],"category_scores_gemma":[0.0003399341,0.0001344014,0.0002544544,0.0002769278,0.0006859472,0.0001480441,0.0003404428,0.0003214617,0.0003630714],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002046251,"about_ca_system_score_gemma":0.0001849411,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0005122147,"about_ca_topic_score_gemma":0.0003226078,"domain_scores_codex":[0.9998705,0.00002078973,0.00002221113,0.00003841917,0.00002039425,0.00002765061],"domain_scores_gemma":[0.9998077,0.00004425944,0.00007086398,0.00001426313,0.0000140413,0.00004886931],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.002043527,0.0004067118,0.08783438,0.0003437207,0.0002243418,0.04575748,0.000443075,0.0004567523,0.8485532,0.0008081988,0.0007723195,0.01235627],"study_design_scores_gemma":[0.0006773724,0.003113608,0.303599,0.0001517388,0.0005883638,0.4524204,0.0005510782,0.002134304,0.2262851,0.0006622999,0.009761916,0.00005486479],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.997664,0.0002260997,0.0007793204,0.00006198511,0.000009465489,0.00002425553,0.0001748982,0.00004543872,0.001014569],"genre_scores_gemma":[0.9985822,0.0001040885,0.0006933196,0.00003386296,0.0000117072,0.00001339558,0.0002171395,0.000008983656,0.0003353009],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003208663,"threshold_uncertainty_score":0.01073408,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0112920443754644,"score_gpt":0.2469046590338616,"score_spread":0.2356126146583972,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}