{"id":"W2125518260","doi":"10.1093/rheumatology/keq218","title":"Successful treatment of severe paediatric rheumatic disease-associated macrophage activation syndrome with interleukin-1 inhibition following conventional immunosuppressive therapy: case series with 12 patients","year":2010,"lang":"en","type":"letter","venue":"Lara D. Veeken","topic":"Autoimmune and Inflammatory Disorders Research","field":"Medicine","cited_by":283,"is_retracted":false,"has_abstract":false,"ca_institutions":"Alberta Children's Hospital; University of Calgary","funders":"","keywords":"Medicine; Macrophage activation syndrome; Disease; Rheumatic disease; Immunology; Interleukin 6; Intensive care medicine; Internal medicine; Cytokine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow"],"consensus_categories":[],"category_scores_codex":[0.0001139485,0.0005400222,0.0009656806,0.0003685709,0.0002257915,0.00007535566,0.0001290662,0.0006795075,0.0003657542],"category_scores_gemma":[0.00006209537,0.0003827343,0.0003211435,0.0003128359,0.0001856344,0.0005107266,0.00004951169,0.001180594,0.00001519369],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003704025,"about_ca_system_score_gemma":0.0005237877,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0002170142,"about_ca_topic_score_gemma":0.00003616024,"domain_scores_codex":[0.9972,0.0002124156,0.0006291008,0.0004921073,0.0009911874,0.000475188],"domain_scores_gemma":[0.9981166,0.0001390242,0.000720687,0.0005407358,0.0003736023,0.0001093091],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.01590769,0.007215224,0.7527679,0.005652215,0.01423365,0.1491633,0.005441926,0.00004931309,0.001462989,0.00001085222,0.03886669,0.009228288],"study_design_scores_gemma":[0.1313669,0.04252467,0.7268643,0.01755125,0.006060392,0.01428621,0.002714303,0.0001841689,0.005207229,0.0002990156,0.04779054,0.00515104],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9904601,0.0004835267,0.000010656,0.006408464,0.0001347183,0.001988048,0.0003186722,0.00007290232,0.0001229129],"genre_scores_gemma":[0.9871854,0.000177265,0.00005809161,0.002476555,0.0001128798,0.0004215868,0.007843333,0.0001331112,0.001591743],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.1348771,"threshold_uncertainty_score":0.9998624,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01009952494476511,"score_gpt":0.2374885991345482,"score_spread":0.2273890741897831,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}