{"id":"W2125518260","doi":"10.1093/rheumatology/keq218","title":"Successful treatment of severe paediatric rheumatic disease-associated macrophage activation syndrome with interleukin-1 inhibition following conventional immunosuppressive therapy: case series with 12 patients","year":2010,"lang":"en","type":"letter","venue":"Lara D. Veeken","topic":"Autoimmune and Inflammatory Disorders Research","field":"Medicine","cited_by":283,"is_retracted":false,"has_abstract":false,"ca_institutions":"Alberta Children's Hospital; University of Calgary","funders":"","keywords":"Medicine; Macrophage activation syndrome; Disease; Rheumatic disease; Immunology; Interleukin 6; Intensive care medicine; Internal medicine; Cytokine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005598157,0.00157233,0.001435581,0.0005659959,0.00157039,0.0009716168,0.001086578,0.004372467,0.001003767],"category_scores_gemma":[0.004078613,0.0006255619,0.001472823,0.0005921128,0.001613895,0.0007618117,0.00106471,0.002034335,0.0004843497],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0007885134,"about_ca_system_score_gemma":0.0008125319,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0008524724,"about_ca_topic_score_gemma":0.0009755024,"domain_scores_codex":[0.9990472,0.0002421006,0.0001460299,0.0001414386,0.0001337699,0.0002894184],"domain_scores_gemma":[0.9982725,0.0007596487,0.0003015732,0.0001743301,0.00008192713,0.0004100484],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0001103412,0.0001241536,0.01531508,0.00004763712,0.00003795819,0.9777711,0.0002846658,0.0001787814,0.001140357,0.0001406962,0.0004596462,0.004389693],"study_design_scores_gemma":[0.00007463672,0.0005510222,0.01218906,0.00001734784,0.00002895941,0.9849635,0.0001489885,0.0002250026,0.0007021531,0.0001173726,0.0009631477,0.00001889437],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9814101,0.004585979,0.003071259,0.002414858,0.0004472626,0.0001440922,0.0001436899,0.0001066775,0.007676017],"genre_scores_gemma":[0.99431,0.001630163,0.001306499,0.0009244576,0.0005187303,0.00007336344,0.0001067043,0.00003151662,0.001098555],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.004372467,"threshold_uncertainty_score":0.005721092,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01009952494476511,"score_gpt":0.2374885991345482,"score_spread":0.2273890741897831,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}