{"id":"W2127778928","doi":"10.1001/jamaneurol.2013.4408","title":"Natural History of Huntington Disease","year":2013,"lang":"en","type":"article","venue":"JAMA Neurology","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":120,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Huntington's disease; Chorea; Disease; Rating scale; Internal medicine; Medicine; Cohort; Prospective cohort study; Psychology; Physical therapy","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005445674,0.0001256137,0.000258333,0.0004031667,0.0004589038,0.0004332276,0.0003507379,0.0004598592,0.001063196],"category_scores_gemma":[0.001932503,0.0001389571,0.0001750442,0.000344255,0.0005510027,0.0005060471,0.0003175151,0.0006783918,0.0001755001],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0007662461,"about_ca_system_score_gemma":0.0006554773,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.009137045,"about_ca_topic_score_gemma":0.007598625,"domain_scores_codex":[0.9996513,0.0001165409,0.00002463221,0.00009506072,0.00007953619,0.00003298207],"domain_scores_gemma":[0.9990267,0.0001560443,0.0003967012,0.00005813315,0.0001594655,0.0002030181],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0001152139,0.00004752791,0.9857392,0.00003622978,0.00007501474,0.0004208911,0.0001175462,0.0001350238,0.0004582209,0.0003264996,0.0009455151,0.01158327],"study_design_scores_gemma":[0.000007166186,0.00009128873,0.9964368,0.00003395466,0.00002144332,0.00143687,0.00007174312,0.0002270323,0.00005134541,0.0004963735,0.001120058,0.000006001384],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9776709,0.01263159,0.0007209494,0.002245398,0.00008068788,0.00005483242,0.001317323,0.00002376741,0.005254598],"genre_scores_gemma":[0.9966097,0.001552876,0.00024757,0.0003396896,0.00007490702,0.00001689723,0.0007185412,0.000002772714,0.0004369765],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.009137045,"threshold_uncertainty_score":0.01816767,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01701522957846978,"score_gpt":0.2285332187758257,"score_spread":0.211517989197356,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}