{"id":"W2131432191","doi":"10.1002/pbc.22023","title":"Initial presentation of unscreened children with sickle cell disease: The Toronto experience","year":2009,"lang":"en","type":"article","venue":"Pediatric Blood & Cancer","topic":"Hemoglobinopathies and Related Disorders","field":"Medicine","cited_by":12,"is_retracted":false,"has_abstract":true,"ca_institutions":"SickKids Foundation; Hospital for Sick Children; University of British Columbia; University of Toronto; McMaster University","funders":"","keywords":"Medicine; Pediatrics; Acute chest syndrome; Disease; Population; Sepsis; Newborn screening; Retrospective cohort study; Sickle cell anemia; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002928243,0.0004278488,0.0002458819,0.0006775758,0.002149826,0.0008420801,0.0006577276,0.0005566104,0.002451991],"category_scores_gemma":[0.002022684,0.0003462178,0.0002805464,0.001321164,0.001266675,0.0004721552,0.000994368,0.0008817149,0.0002113583],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.007434912,"about_ca_system_score_gemma":0.005231874,"about_ca_topic_candidate":true,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.398086,"about_ca_topic_score_gemma":0.5734189,"domain_scores_codex":[0.9994387,0.00006126283,0.00005575917,0.00006328159,0.0001630643,0.0002178758],"domain_scores_gemma":[0.9981347,0.0001975728,0.0005023765,0.00005276766,0.0002295923,0.0008828425],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00004946128,0.00006295583,0.9527314,0.00008154086,0.00001988853,0.03251591,0.007538083,0.0001043189,0.0006186819,0.0002026561,0.00169,0.004385072],"study_design_scores_gemma":[0.00001020363,0.000186778,0.9450038,0.0001219976,0.00002570794,0.04136697,0.01040316,0.0001475448,0.0002245209,0.00005713062,0.002428934,0.00002324469],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9955154,0.0009382038,0.00003380036,0.0003575261,0.00002330591,0.00002282601,0.0001959745,0.000009788589,0.002903249],"genre_scores_gemma":[0.9987091,0.00068233,0.00005250929,0.0001263886,0.00001309871,0.000005980475,0.0001229381,0.00000327803,0.0002843524],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.601914,"threshold_uncertainty_score":0.7915378,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.00658528673061074,"score_gpt":0.2644964659387304,"score_spread":0.2579111792081196,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}