{"id":"W2135867317","doi":"10.4021//jmc.v2i4.221","title":"Rapidly Progressive Creutzfeldt-Jakob Disease VV1 Subtype","year":2011,"lang":"en","type":"article","venue":"Journal of Medical Cases","topic":"Prion Diseases and Protein Misfolding","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Medicine; Brain biopsy; Pathology; Dementia; Disease; Magnetic resonance imaging; Encephalopathy; Creutzfeldt-Jakob Syndrome; Central nervous system; Personality changes; Prion protein; Internal medicine; Radiology","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.000135407,0.0005036828,0.0002678552,0.0005052107,0.0005539295,0.0003433268,0.0002649773,0.0005666726,0.001245718],"category_scores_gemma":[0.0004850196,0.0001489112,0.0001996294,0.0002665206,0.0002498378,0.0002701985,0.0002473904,0.0003338276,0.0005450932],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002738028,"about_ca_system_score_gemma":0.0001664652,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001850979,"about_ca_topic_score_gemma":0.001959828,"domain_scores_codex":[0.9998916,0.00001286229,0.000008620635,0.00002240409,0.00002684921,0.00003769312],"domain_scores_gemma":[0.9998857,0.00001710752,0.00005122441,0.00001050341,0.00001065332,0.00002478093],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0005987013,0.00038839,0.2159166,0.0003535157,0.0000741371,0.6813372,0.00173593,0.000325723,0.05347463,0.002791564,0.00404826,0.03895543],"study_design_scores_gemma":[0.00003653297,0.0003037016,0.1200127,0.00005322998,0.00003017572,0.8673773,0.0002744437,0.0004186216,0.00479591,0.000741502,0.00593912,0.00001677033],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9910075,0.001814953,0.0005301089,0.0001700864,0.00003012054,0.00004030209,0.0001486002,0.00004056375,0.006217857],"genre_scores_gemma":[0.9977602,0.0004719001,0.000166291,0.0000747863,0.00003851501,0.000003601865,0.00008699969,0.000006827939,0.001390744],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001850979,"threshold_uncertainty_score":0.004167318,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02909858416154289,"score_gpt":0.2979467325136756,"score_spread":0.2688481483521327,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}