{"id":"W2135908745","doi":"10.5214/ans.0972.7531.210308","title":"The mechanism of degeneration of striatal neuronal subtypes in Huntington disease","year":2014,"lang":"en","type":"review","venue":"Annals of Neurosciences","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":65,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of Alberta Hospital; Health Research Foundation; Douglas Mental Health University Institute; McGill University","funders":"","keywords":"Huntington's disease; Neurodegeneration; Striatum; Neuroscience; Degeneration (medical); Neuronal degeneration; Medium spiny neuron; Mechanism (biology); Pathological; Biology; Basal ganglia; Disease; Medicine; Pathology; Central nervous system; Dopamine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow"],"consensus_categories":[],"category_scores_codex":[0.0006887463,0.0003702719,0.001060032,0.000343513,0.0001590037,0.00005819906,0.00140124,0.00007297753,0.00000598102],"category_scores_gemma":[0.004723739,0.0002519227,0.0004611855,0.001043734,0.0008849962,0.0001624992,0.0002577084,0.0001944649,0.000002791155],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000004880268,"about_ca_system_score_gemma":0.0005279525,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00001430034,"about_ca_topic_score_gemma":0.00001342836,"domain_scores_codex":[0.9952133,0.001287422,0.001297374,0.000810514,0.0009867342,0.0004046279],"domain_scores_gemma":[0.9959893,0.001520374,0.001571051,0.0006327197,0.0001442268,0.0001422999],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.0003268661,0.002306462,0.0006796886,0.02323929,0.00003377628,0.00001808607,0.0002027913,0.001172968,0.3185312,0.1105176,0.0006998885,0.5422714],"study_design_scores_gemma":[0.000214259,0.0007545149,0.0008332785,0.002073661,0.0001572071,0.000002047806,0.00001437257,0.0003255253,0.9303865,0.001636393,0.06308674,0.0005154453],"study_design_candidate":"bench_or_experimental","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.3835917,0.6100063,0.00007062226,0.0003247377,0.003040389,0.001990485,0.000725406,0.00003663306,0.0002136649],"genre_scores_gemma":[0.2236014,0.7760832,0.00001065416,0.0001002512,0.00007174279,0.00003478741,0.000004954808,0.00002519703,0.00006779782],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.6118553,"threshold_uncertainty_score":0.9999933,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.1398139474453098,"score_gpt":0.3734594521490934,"score_spread":0.2336455047037836,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}