{"id":"W2143584019","doi":"10.4187/aarc0427","title":"Cystic Fibrosis: Pathogenesis and Future Treatment Strategies","year":2009,"lang":"en","type":"review","venue":"Respiratory Care","topic":"Cystic Fibrosis Research Advances","field":"Medicine","cited_by":182,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hospital for Sick Children","funders":"","keywords":"Cystic fibrosis; Medicine; Disease; Pathogenesis; Cystic fibrosis transmembrane conductance regulator; Pathophysiology; Fibrosis; Lung; Inflammation; Bioinformatics; Intensive care medicine; Immunology; Pathology; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0009404353,0.0009107323,0.001414735,0.00196564,0.0004098924,0.00101068,0.000995977,0.001815052,0.006264886],"category_scores_gemma":[0.0008052936,0.0002002592,0.0005948538,0.0009170054,0.0005603421,0.001583138,0.0007624083,0.002618316,0.002977054],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0008113563,"about_ca_system_score_gemma":0.001053454,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0007877902,"about_ca_topic_score_gemma":0.002117549,"domain_scores_codex":[0.9997321,0.00006988118,0.00003209555,0.0000369102,0.0001036625,0.00002534631],"domain_scores_gemma":[0.9996948,0.0001190661,0.00004148797,0.00001224304,0.00008359575,0.00004886482],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0001102543,0.0002686693,0.0002069466,0.005350996,0.00005616571,0.0008671524,0.00006871008,0.0005788367,0.001849373,0.006742502,0.0451888,0.9387115],"study_design_scores_gemma":[0.00008888148,0.0002955999,0.001296725,0.006354951,0.00009773672,0.004460936,0.0001868998,0.0003303455,0.0005532291,0.00906213,0.9772379,0.00003474189],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.0001481672,0.9951479,0.0003241433,0.002064326,0.0004116779,0.000008486906,0.00001257005,0.00001502031,0.00186771],"genre_scores_gemma":[0.0009709933,0.9955412,0.0007640892,0.0007351303,0.0006731014,0.00001869592,0.00002820586,0.000002444202,0.00126616],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.006264886,"threshold_uncertainty_score":0.02095819,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03759178027862448,"score_gpt":0.3660786932478184,"score_spread":0.328486912969194,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}