{"id":"W2153733523","doi":"10.1086/315197","title":"Partial Interferon‐γ Receptor Signaling Chain Deficiency in a Patient with Bacille Calmette‐Guérin and<i>Mycobacterium abscessus</i>Infection","year":2000,"lang":"en","type":"article","venue":"The Journal of Infectious Diseases","topic":"Immunodeficiency and Autoimmune Disorders","field":"Immunology and Microbiology","cited_by":175,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"National Cancer Institute; National Institute of Allergy and Infectious Diseases; Centre hospitalier universitaire Sainte-Justine","keywords":"Mycobacterium bovis; Immunology; Interferon gamma; Biology; Nontuberculous mycobacteria; Interferon; Mycobacterium abscessus; Flow cytometry; Mycobacterium; Receptor; Immunodeficiency; Microbiology; Cytokine; Medicine; Immune system; Tuberculosis; Mycobacterium tuberculosis; Pathology; Bacteria; Genetics","routes":{"ca_aff":false,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002952852,0.001641844,0.0009202321,0.001282767,0.002074636,0.0007695793,0.0006622088,0.002843132,0.001792632],"category_scores_gemma":[0.001647001,0.0009267124,0.0005474162,0.0007574337,0.001255985,0.0008250499,0.000659934,0.001853275,0.0004189734],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0007540025,"about_ca_system_score_gemma":0.0006468919,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00357514,"about_ca_topic_score_gemma":0.002946053,"domain_scores_codex":[0.9996303,0.00004304336,0.00003665886,0.0001147205,0.00004418265,0.0001310234],"domain_scores_gemma":[0.9993663,0.0001997121,0.00009132158,0.00003701656,0.00003800277,0.0002675493],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0003876321,0.0001268255,0.04123024,0.00005554877,0.000032926,0.9467106,0.0006756879,0.0001493064,0.007596999,0.0002886766,0.0004579043,0.002287633],"study_design_scores_gemma":[0.00004645108,0.0003522475,0.04183186,0.00002704664,0.0000457056,0.9544235,0.0002132788,0.0003536973,0.001866095,0.0002039333,0.0006121208,0.00002407751],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9947752,0.0007239386,0.000540572,0.0008071186,0.00006064842,0.00005043967,0.0001599355,0.00005285523,0.002829312],"genre_scores_gemma":[0.9988229,0.0002057472,0.0001938835,0.0002265692,0.00005952015,0.000006996109,0.00006368259,0.000009150806,0.000411633],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.00357514,"threshold_uncertainty_score":0.007108688,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.003859980403656946,"score_gpt":0.1926017487138459,"score_spread":0.188741768310189,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}