{"id":"W2154610817","doi":"10.3324/haematol.2011.049676","title":"Development and validation of a predictive model for death in acquired severe ADAMTS13 deficiency-associated idiopathic thrombotic thrombocytopenic purpura: the French TMA Reference Center experience","year":2012,"lang":"en","type":"article","venue":"Haematologica","topic":"Complement system in diseases","field":"Immunology and Microbiology","cited_by":155,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hotel Dieu Hospital","funders":"Etablissement Français du Sang; GIS-Institut des Maladies Rares","keywords":"ADAMTS13; Thrombotic thrombocytopenic purpura; Medicine; Purpura (gastropod); Thrombocytopenic purpura; Internal medicine; Immunology; Pediatrics; Platelet","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005226068,0.0001987941,0.0004652143,0.00006254471,0.0002367548,0.00001267361,0.000317189,0.0001675948,0.0000683278],"category_scores_gemma":[0.0002689318,0.0001335671,0.00004942327,0.0001288617,0.0001821717,0.0001817707,0.0002055522,0.00009094751,0.00001307355],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000098524,"about_ca_system_score_gemma":0.0001032053,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00003753443,"about_ca_topic_score_gemma":0.00007971562,"domain_scores_codex":[0.9983245,0.0002767027,0.0005486386,0.0003064432,0.00008191089,0.0004617776],"domain_scores_gemma":[0.9991003,0.0002095905,0.0003067908,0.0002590629,0.00009711443,0.00002711252],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0004321751,0.002108568,0.9002657,0.0004354739,0.0002887994,0.000004685037,0.05898143,0.000332017,0.02532609,0.01044243,0.0007771954,0.0006054246],"study_design_scores_gemma":[0.002993295,0.0002991657,0.9570342,0.0006016853,0.000122205,0.0001622889,0.00549436,0.001684875,0.02986648,0.001057767,0.0001567801,0.000526847],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9947265,0.002000995,0.001703436,0.00004301864,0.0001263822,0.001047053,0.00007827818,0.00004050276,0.0002338207],"genre_scores_gemma":[0.9989474,0.00002398137,0.0003460989,0.00003426486,0.000003394487,0.0005010965,0.00008454432,0.000008856001,0.00005040121],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.05676854,"threshold_uncertainty_score":0.5446708,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.08371613946296001,"score_gpt":0.2979102285476568,"score_spread":0.2141940890846968,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}