{"id":"W2161480369","doi":"10.1136/jnnp-2011-301530","title":"Absence of consensus in diagnostic criteria for familial neurodegenerative diseases","year":2012,"lang":"en","type":"article","venue":"Journal of Neurology Neurosurgery & Psychiatry","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":75,"is_retracted":false,"has_abstract":true,"ca_institutions":"Trinity College","funders":"","keywords":"Amyotrophic lateral sclerosis; Disease; Medicine; Consensus conference; Degenerative disease; Pathology; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005513029,0.0002226972,0.0007806547,0.0004178262,0.00005189039,0.00001034154,0.000179927,0.0001393485,0.00005654013],"category_scores_gemma":[0.003674761,0.0001812204,0.0003470349,0.000309773,0.0002895937,0.0001426681,0.000057178,0.0006134377,0.0000036947],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00001859452,"about_ca_system_score_gemma":0.0003345208,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00000703447,"about_ca_topic_score_gemma":0.000003288702,"domain_scores_codex":[0.9970767,0.0004791561,0.00120734,0.0002506229,0.0003968317,0.0005892945],"domain_scores_gemma":[0.9957561,0.00270062,0.0006111304,0.0002774699,0.0002823232,0.0003723309],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.003734288,0.001023043,0.935398,0.0001258661,0.0000398814,0.0001969299,0.00006251469,0.00006131107,0.04768925,0.00009370155,0.01125619,0.0003190489],"study_design_scores_gemma":[0.001868267,0.001981154,0.9932044,0.00008220359,0.00008005294,0.001038635,0.00001168799,0.0001259144,0.0004094491,0.0002340743,0.0008493126,0.000114913],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.982706,0.001091888,0.00003970393,0.01065755,0.005038177,0.0003857193,0.0000437259,0.00001078343,0.0000264797],"genre_scores_gemma":[0.9944816,0.000356164,0.000376107,0.003372437,0.001332327,0.00001573692,0.000003105336,0.00004190265,0.00002064936],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.05780636,"threshold_uncertainty_score":0.7389954,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03741234551486505,"score_gpt":0.33433249529917,"score_spread":0.296920149784305,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}