{"id":"W2161509813","doi":"10.1016/j.cjca.2010.12.035","title":"Myocardial Alterations in the Murine Model of Fabry Disease Can Be Reversed by Enzyme Replacement Therapy","year":2011,"lang":"en","type":"article","venue":"Canadian Journal of Cardiology","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":7,"is_retracted":false,"has_abstract":false,"ca_institutions":"","funders":"National Institutes of Health; Universidad Nacional de La Plata","keywords":"Medicine; Contractility; Enzyme replacement therapy; Globotriaosylceramide; Fabry disease; Internal medicine; Heart failure; Endocrinology; Cardiology; Myocyte; Contraction (grammar); Vacuolization; Urology; Disease","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004288431,0.001039222,0.0007508784,0.0008560834,0.0003342034,0.0005769911,0.0005028857,0.001176741,0.001519877],"category_scores_gemma":[0.0004314988,0.0003377696,0.0005360339,0.0002864059,0.0007399755,0.0006555108,0.0002353671,0.001466415,0.00044936],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004159826,"about_ca_system_score_gemma":0.0003811117,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0006674111,"about_ca_topic_score_gemma":0.0009254276,"domain_scores_codex":[0.9997557,0.00005708453,0.00003246443,0.00004120949,0.00004849402,0.00006509692],"domain_scores_gemma":[0.9995587,0.00006401898,0.0001593476,0.00006996421,0.0000285338,0.0001195116],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.003412337,0.0003564782,0.0004086249,0.00009373904,0.00004012996,0.000929127,0.00004460371,0.0003702682,0.9901035,0.0005966126,0.0002481346,0.003396525],"study_design_scores_gemma":[0.0009465758,0.005632977,0.008061929,0.00006649733,0.0001900632,0.002352786,0.000136034,0.002508475,0.9746599,0.0008141955,0.004590537,0.00003995226],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9905647,0.002551102,0.002891699,0.0006198865,0.0002002219,0.00007295443,0.0007103057,0.0002427806,0.002146314],"genre_scores_gemma":[0.9926966,0.001376214,0.001738684,0.0001377865,0.00004497604,0.00007499113,0.0006224646,0.00004800128,0.003260363],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001519877,"threshold_uncertainty_score":0.005084515,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.05945617396260583,"score_gpt":0.2821540499804795,"score_spread":0.2226978760178737,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}