{"id":"W2161714187","doi":"10.1212/wnl.0b013e3182735c8b","title":"Child Neurology: Krabbe disease","year":2012,"lang":"en","type":"article","venue":"Neurology","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":6,"is_retracted":false,"has_abstract":true,"ca_institutions":"BC Children's Hospital","funders":"BC Children's Hospital; Faculty of Medicine, University of British Columbia","keywords":"Krabbe disease; Leukodystrophy; Medicine; Neurology; Disease; Pediatrics; Gaucher's disease; White matter; Glucocerebrosidase; Pathology; Psychiatry; Magnetic resonance imaging","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003133113,0.0008995879,0.000686195,0.0009974464,0.001265248,0.0008279431,0.0004605403,0.002140472,0.01711401],"category_scores_gemma":[0.001298331,0.0001589302,0.0002077052,0.001340877,0.0008362318,0.0008945466,0.0007579239,0.001563485,0.003859055],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001290295,"about_ca_system_score_gemma":0.00120844,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.008562442,"about_ca_topic_score_gemma":0.01044501,"domain_scores_codex":[0.999684,0.00005375267,0.00003737583,0.00004488592,0.00008845734,0.00009150136],"domain_scores_gemma":[0.9995946,0.0001194353,0.00009806888,0.00001879395,0.00007044967,0.00009863521],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0001905512,0.000216801,0.04461668,0.0007260452,0.00008369845,0.7377634,0.0005276178,0.0003798418,0.002441921,0.00900636,0.1126129,0.09143427],"study_design_scores_gemma":[0.00002282468,0.00004576673,0.02026258,0.0004153767,0.00003010445,0.9096657,0.0002106738,0.00009804522,0.0003210551,0.002063536,0.06684766,0.00001668953],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"other","genre_gemma":"empirical","genre_scores_codex":[0.2290446,0.197353,0.00612962,0.07517996,0.005200393,0.0003317714,0.002396115,0.001025193,0.4833394],"genre_scores_gemma":[0.7677705,0.1168587,0.004437721,0.02715221,0.007737087,0.0001402679,0.001750722,0.0003394748,0.07381332],"genre_candidate":"empirical","genre_consensus":null,"teacher_disagreement_score":0.01711401,"threshold_uncertainty_score":0.05725205,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.020926455324174,"score_gpt":0.2961152789168309,"score_spread":0.2751888235926569,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}