{"id":"W2162912209","doi":"10.1093/brain/awh263","title":"Action myoclonus-renal failure syndrome: characterization of a unique cerebro-renal disorder","year":2004,"lang":"en","type":"article","venue":"Brain","topic":"Glycogen Storage Diseases and Myoclonus","field":"Medicine","cited_by":98,"is_retracted":false,"has_abstract":true,"ca_institutions":"Montreal Neurological Institute and Hospital","funders":"Canadian Institutes of Health Research","keywords":"Medicine; Myoclonus; Proteinuria; Dialysis; Focal segmental glomerulosclerosis; Nephrotic syndrome; Internal medicine; Autopsy; Pediatrics; Pathology; Kidney; Anesthesia","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00008387344,0.0001596139,0.0002598729,0.0001343495,0.00005794444,0.00001341229,0.00006796901,0.0001216754,0.0003110035],"category_scores_gemma":[0.00006861563,0.0001437266,0.0001416982,0.0002766938,0.00005410363,0.0001351587,0.00002576961,0.0001398397,0.00004107007],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00007640263,"about_ca_system_score_gemma":0.0001884706,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0001443334,"about_ca_topic_score_gemma":0.00004557545,"domain_scores_codex":[0.999001,0.00003332998,0.000261944,0.0002350951,0.000251739,0.0002169261],"domain_scores_gemma":[0.9993464,0.00001606813,0.0001333532,0.0002431583,0.0001027853,0.0001581994],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.0003686421,0.0004220288,0.001843706,0.0002389795,0.0001438105,0.0009204902,0.000323862,0.00005687024,0.9825065,0.001368841,0.0004901426,0.01131617],"study_design_scores_gemma":[0.0175548,0.002375043,0.6889125,0.001476309,0.0007529974,0.009676975,0.000638194,0.000267871,0.1146987,0.00110485,0.1613747,0.001167058],"study_design_candidate":"bench_or_experimental","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9888883,0.0000478955,0.00595025,0.004327727,0.00009048976,0.0003972373,0.00006922401,0.00007558077,0.0001533209],"genre_scores_gemma":[0.9972441,0.00001663323,0.0004893859,0.0005862146,0.0001385325,0.0000298979,0.0005090554,0.00003079906,0.0009554091],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.8678077,"threshold_uncertainty_score":0.5861,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01014392315166551,"score_gpt":0.2537377546859028,"score_spread":0.2435938315342372,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}