{"id":"W2163318706","doi":"10.1093/rheumatology/ker397","title":"Musculoskeletal manifestations of mucopolysaccharidoses","year":2011,"lang":"en","type":"review","venue":"Lara D. Veeken","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":103,"is_retracted":false,"has_abstract":true,"ca_institutions":"BC Children's Hospital","funders":"BioMarin Pharmaceutical","keywords":"Medicine; Lysosomal storage disorders; Enzyme replacement therapy; Muscle contracture; Mucopolysaccharidosis; Arthritis; Disease; Joint disease; Intensive care medicine; Joint Contracture; Contracture; Surgery; Pathology; Immunology; Osteoarthritis; Alternative medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003442224,0.001253975,0.001573358,0.002770196,0.0003431899,0.0008903378,0.000615689,0.001147161,0.003441005],"category_scores_gemma":[0.0007624511,0.0002316239,0.0004907383,0.001958965,0.0004992192,0.0008843855,0.0006576324,0.0008511064,0.001929863],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005088283,"about_ca_system_score_gemma":0.0007429438,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001321931,"about_ca_topic_score_gemma":0.001741632,"domain_scores_codex":[0.9997386,0.00004856378,0.00004810825,0.00005033736,0.00008388492,0.0000304585],"domain_scores_gemma":[0.9997323,0.00009969177,0.00006464372,0.00001112098,0.00006483492,0.0000274296],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00009915552,0.00004766222,0.0008776105,0.01392109,0.000139952,0.005333198,0.0001363705,0.0002588342,0.002548896,0.00182696,0.03886537,0.9359449],"study_design_scores_gemma":[0.00005707125,0.0001513524,0.006755874,0.01021349,0.0002646395,0.0990117,0.0002772037,0.0001298726,0.001303875,0.001931359,0.8798529,0.00005077901],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.0004126157,0.9971066,0.000136182,0.0002020563,0.0001499692,0.000005328548,0.00002204264,0.00001233825,0.001952805],"genre_scores_gemma":[0.005005063,0.9928402,0.0002488337,0.0002760892,0.0002974976,0.000007235464,0.00005773406,0.000002448911,0.001265007],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.003441005,"threshold_uncertainty_score":0.01151133,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.06907878756538768,"score_gpt":0.3799261471693886,"score_spread":0.3108473596040009,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}