{"id":"W2170325262","doi":"10.1165/rcmb.2007-0036oc","title":"Fenretinide Corrects Newly Found Ceramide Deficiency in Cystic Fibrosis","year":2007,"lang":"en","type":"article","venue":"American Journal of Respiratory Cell and Molecular Biology","topic":"Sphingolipid Metabolism and Signaling","field":"Biochemistry, Genetics and Molecular Biology","cited_by":108,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; Montreal General Hospital","funders":"","keywords":"Ceramide; Fenretinide; Cystic fibrosis; Knockout mouse; Sphingolipid; Biology; Medicine; Lipid signaling; Internal medicine; Endocrinology; Cancer research; Immunology; Retinoid; Inflammation; Biochemistry; Apoptosis; Receptor","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002093964,0.0004412142,0.0006143171,0.0003983122,0.000190946,0.0002444686,0.0003080845,0.0006260145,0.0006148273],"category_scores_gemma":[0.0002556384,0.0001268607,0.0003193546,0.0001521599,0.0002881385,0.000225877,0.0002159838,0.0006216451,0.0001536391],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002198638,"about_ca_system_score_gemma":0.0002370374,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0005443671,"about_ca_topic_score_gemma":0.000806977,"domain_scores_codex":[0.9998307,0.00003162314,0.00002726545,0.00003076141,0.00005480171,0.00002476633],"domain_scores_gemma":[0.9998925,0.00002277822,0.00003263738,0.000008059788,0.00001603385,0.00002791123],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.000716638,0.00009012146,0.0009337232,0.00007444092,0.00002027879,0.00121985,0.00003154384,0.0001110451,0.9866431,0.00004776939,0.0000885959,0.010023],"study_design_scores_gemma":[0.0002793002,0.00339415,0.0255809,0.00004273411,0.0001475163,0.01112379,0.0001223049,0.001680545,0.9484903,0.0001610644,0.008952756,0.00002463198],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.994449,0.003132354,0.00130683,0.0002273773,0.00004647049,0.00003874639,0.0001432621,0.0001048341,0.0005511515],"genre_scores_gemma":[0.9930634,0.002062468,0.003087796,0.0001391861,0.00003595114,0.00003701849,0.0002603778,0.00002588219,0.001287846],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.0006260145,"threshold_uncertainty_score":0.002056777,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.005828089068506313,"score_gpt":0.2560233270853969,"score_spread":0.2501952380168906,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}