{"id":"W2174005269","doi":"10.1186/s13041-015-0168-0","title":"Human induced pluripotent stem cell derived neurons as a model for Williams-Beuren syndrome","year":2015,"lang":"en","type":"article","venue":"Molecular Brain","topic":"Williams Syndrome Research","field":"Neuroscience","cited_by":46,"is_retracted":false,"has_abstract":true,"ca_institutions":"St. Michael's Hospital; SickKids Foundation; University of Toronto; Hospital for Sick Children","funders":"Canadian Institutes of Health Research; Hospital for Sick Children","keywords":"Induced pluripotent stem cell; Neuroscience; Excitatory postsynaptic potential; Biology; Neurotransmitter receptor; Neurotransmission; Glutamatergic; Neurotransmitter; Cell biology; Gene; Glutamate receptor; Receptor; Embryonic stem cell; Genetics; Inhibitory postsynaptic potential","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002537104,0.0004422526,0.0002748393,0.0004492092,0.0001599947,0.0002283666,0.0002901982,0.0004592735,0.001147946],"category_scores_gemma":[0.0001594086,0.0001403101,0.0002268555,0.000278284,0.0003654223,0.0001555049,0.0002857137,0.0005700426,0.0004022503],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000191357,"about_ca_system_score_gemma":0.0001705563,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0003455619,"about_ca_topic_score_gemma":0.0005605641,"domain_scores_codex":[0.9998139,0.00003161045,0.00003402759,0.00003597198,0.0000678109,0.00001675992],"domain_scores_gemma":[0.9999132,0.00002387337,0.00002254696,0.00001573641,0.00001065893,0.00001400082],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.0002606503,0.0001008347,0.0009760462,0.0001039336,0.00002937346,0.0009920821,0.00007955234,0.0005526858,0.9926704,0.0008054873,0.0002120758,0.003216774],"study_design_scores_gemma":[0.0001597112,0.002504061,0.01300407,0.00007698988,0.0002463258,0.006740331,0.0001940367,0.005197437,0.9548379,0.00110371,0.01590713,0.00002840444],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9822636,0.001864382,0.01127682,0.0001552068,0.00009245992,0.0003156996,0.001665391,0.0001300325,0.00223642],"genre_scores_gemma":[0.9829474,0.002171147,0.009047368,0.00008892603,0.00001508293,0.0003379808,0.002651055,0.00003497741,0.002706003],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001147946,"threshold_uncertainty_score":0.003840268,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.09615566350055497,"score_gpt":0.3254935494304502,"score_spread":0.2293378859298952,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}