{"id":"W2302814439","doi":"10.3174/ajnr.a4719","title":"Reduced Myelin Water in the White Matter Tracts of Patients with Niemann-Pick Disease Type C","year":2016,"lang":"en","type":"article","venue":"American Journal of Neuroradiology","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":19,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of British Columbia; University of British Columbia Hospital","funders":"","keywords":"White matter; Diffusion MRI; Myelin; Medicine; Niemann–Pick disease; Pathology; Disease; Neuroscience; Magnetic resonance imaging; Internal medicine; Radiology; Central nervous system; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003441894,0.000585334,0.0004977251,0.001584934,0.0007676398,0.0005712438,0.0002614749,0.0008141447,0.001152604],"category_scores_gemma":[0.002899759,0.0002391849,0.0002025406,0.0007742203,0.0006345321,0.0005046086,0.0003067647,0.0003312537,0.0001852936],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003773288,"about_ca_system_score_gemma":0.000323307,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.004612435,"about_ca_topic_score_gemma":0.003527979,"domain_scores_codex":[0.9997693,0.00003476942,0.00004542405,0.00006441687,0.00005262036,0.00003347849],"domain_scores_gemma":[0.9993145,0.0001707946,0.0002297944,0.00003936849,0.0001029855,0.000142558],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001336221,0.0001583359,0.9568663,0.00007545059,0.0001184458,0.01268171,0.001553723,0.0002500386,0.02047642,0.0001028435,0.000236697,0.006143861],"study_design_scores_gemma":[0.00005025811,0.0003829237,0.9795887,0.0000129568,0.00005827497,0.01701121,0.0007398226,0.0003709816,0.001346997,0.0001566744,0.0002574034,0.00002388349],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9996094,0.00009290054,0.00004437601,0.00003042327,0.000003066854,0.000004139516,0.00003665869,0.000004524759,0.0001744452],"genre_scores_gemma":[0.9997432,0.00005058137,0.00007487307,0.00002464721,0.000007558999,0.000003518877,0.00004070274,0.000002716707,0.00005223639],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.004612435,"threshold_uncertainty_score":0.009171188,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01180493204937516,"score_gpt":0.2650335237782135,"score_spread":0.2532285917288384,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}