{"id":"W2303291360","doi":"10.1007/s00223-016-0110-1","title":"Osteogenesis Imperfecta Type VI in Individuals from Northern Canada","year":2016,"lang":"en","type":"article","venue":"Calcified Tissue International","topic":"Connective tissue disorders research","field":"Biochemistry, Genetics and Molecular Biology","cited_by":36,"is_retracted":false,"has_abstract":false,"ca_institutions":"Shriners Hospitals for Children - Canada; McGill University; Children's Hospital of Eastern Ontario","funders":"Fonds de Recherche du Québec - Santé; Alexion Pharmaceuticals; Amgen","keywords":"Osteogenesis imperfecta; Osteoid; Osteoclast; Internal medicine; PEDF; Endocrinology; Dentinogenesis imperfecta; Osteoporosis; Nephrocalcinosis; Bone mineral; Medicine; RANKL; Chemistry; Anatomy","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002565751,0.0005544189,0.0007417879,0.002523496,0.005832742,0.001343461,0.001131432,0.0006201274,0.003691466],"category_scores_gemma":[0.001354504,0.0004563187,0.0005354824,0.004812346,0.0009657398,0.0002571481,0.001026478,0.0007032808,0.0004358435],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.01018486,"about_ca_system_score_gemma":0.0111775,"about_ca_topic_candidate":true,"about_ca_topic_consensus":true,"about_ca_topic_score_codex":0.9846837,"about_ca_topic_score_gemma":0.9866751,"domain_scores_codex":[0.9990925,0.00004523069,0.000066593,0.0001802123,0.0002781608,0.0003373487],"domain_scores_gemma":[0.9990872,0.00006040694,0.0001695509,0.00002773256,0.0003737282,0.000281304],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.000104142,0.00004322884,0.986311,0.00003485454,0.00004601734,0.003586869,0.003608597,0.0001013509,0.0007161133,0.0002508823,0.0008051643,0.0043917],"study_design_scores_gemma":[0.00001113748,0.00005003157,0.9877669,0.00006074409,0.00005463436,0.003177766,0.007008394,0.0001402542,0.0001020398,0.00008456135,0.001525241,0.00001830984],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9934804,0.000444282,0.0001066824,0.0001660124,0.00001553615,0.00004008786,0.001506372,0.000007879259,0.004232785],"genre_scores_gemma":[0.9966213,0.0004129769,0.0001525666,0.00009643052,0.00000630643,0.00001703542,0.0005119978,0.000008747333,0.002172659],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01531631,"threshold_uncertainty_score":0.07389665,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01284013146249085,"score_gpt":0.2845396183284304,"score_spread":0.2716994868659395,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}