{"id":"W2303553415","doi":"10.1097/mpg.0000000000000935","title":"Clinical Features of Lysosomal Acid Lipase Deficiency","year":2015,"lang":"en","type":"article","venue":"Journal of Pediatric Gastroenterology and Nutrition","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":115,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hospital for Sick Children","funders":"","keywords":"Medicine; Internal medicine; Gastroenterology; Steatosis; Prospective cohort study","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0008463573,0.00009315884,0.0004119246,0.0003227305,0.00002790856,0.000006344125,0.00009359468,0.000142064,0.0000150868],"category_scores_gemma":[0.0005108551,0.00007340891,0.0001605775,0.000149817,0.0001478333,0.0001175954,0.00004195051,0.0004458779,0.000002405847],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00002797019,"about_ca_system_score_gemma":0.0001073902,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000003903015,"about_ca_topic_score_gemma":0.000003205963,"domain_scores_codex":[0.9984951,0.0001974691,0.0006162824,0.0001240405,0.000350833,0.0002162921],"domain_scores_gemma":[0.998668,0.00006444963,0.0003695344,0.00009580144,0.0004990557,0.0003031798],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.009114745,0.001578256,0.978944,0.0001565459,0.000045213,0.0002195713,0.00007724686,7.223401e-7,0.000377797,0.00001730226,0.008365162,0.001103419],"study_design_scores_gemma":[0.01678036,0.02893787,0.9482256,0.00005091873,0.0004765324,0.003876167,0.0004305426,0.00001013333,0.0002596001,0.0006089599,0.0002753941,0.00006796427],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9924517,0.005429853,0.0002959079,0.001321931,0.0002685107,0.0001337455,0.000005074658,0.000005150262,0.00008814262],"genre_scores_gemma":[0.9946799,0.002411746,0.001692521,0.0001612192,0.001024797,0.000002210469,0.000004397191,0.000007276505,0.00001589894],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.03071846,"threshold_uncertainty_score":0.2993529,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03565195668194703,"score_gpt":0.3354138315702819,"score_spread":0.2997618748883349,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}