{"id":"W2303553415","doi":"10.1097/mpg.0000000000000935","title":"Clinical Features of Lysosomal Acid Lipase Deficiency","year":2015,"lang":"en","type":"article","venue":"Journal of Pediatric Gastroenterology and Nutrition","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":115,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hospital for Sick Children","funders":"","keywords":"Medicine; Internal medicine; Gastroenterology; Steatosis; Prospective cohort study","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004710938,0.0004409222,0.0004116771,0.0007415593,0.0003060948,0.0005691191,0.0002719344,0.0003736316,0.002367219],"category_scores_gemma":[0.001877589,0.0001369547,0.0002276134,0.0007044204,0.0004525662,0.000455546,0.0005780854,0.0003344338,0.0004996512],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003452576,"about_ca_system_score_gemma":0.0005108436,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001210141,"about_ca_topic_score_gemma":0.001365631,"domain_scores_codex":[0.9994386,0.0000961707,0.0001083408,0.0001517024,0.0001005855,0.0001046887],"domain_scores_gemma":[0.9987836,0.0002124892,0.0006466987,0.00003451657,0.0001254816,0.0001970522],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"case_report","study_design_scores_codex":[0.0001126791,0.00001732044,0.98893,0.00003276585,0.00001980676,0.005319699,0.00008192849,0.00005210146,0.001241998,0.00005769675,0.0003491987,0.003784726],"study_design_scores_gemma":[0.00001897322,0.0002267673,0.9197652,0.00006661939,0.00003290545,0.076759,0.0004244866,0.0001677705,0.000910778,0.00007988778,0.001540204,0.00000752812],"study_design_candidate":"case_report","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9943844,0.001767821,0.0004333192,0.000188359,0.00001251861,0.00003409406,0.0006872675,0.00002957299,0.002462685],"genre_scores_gemma":[0.9985018,0.0004416259,0.0003189314,0.0000885128,0.00001937381,0.00001025488,0.0004225801,0.000003214254,0.0001936637],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002367219,"threshold_uncertainty_score":0.007919192,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03565195668194703,"score_gpt":0.3354138315702819,"score_spread":0.2997618748883349,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}