{"id":"W2320645542","doi":"10.1097/nen.0000000000000008","title":"Adult-Onset Leukodystrophy: Review of 3 Clinicopathologic Phenotypes and a Proposed Classification","year":2013,"lang":"en","type":"article","venue":"Journal of Neuropathology & Experimental Neurology","topic":"RNA regulation and disease","field":"Biochemistry, Genetics and Molecular Biology","cited_by":19,"is_retracted":false,"has_abstract":true,"ca_institutions":"London Health Sciences Centre; Western University","funders":"","keywords":"Leukodystrophy; Pathology; Leukoencephalopathy; Autopsy; Krabbe disease; Metachromatic leukodystrophy; Medicine; Abnormality; Confusion; Disease; Biology; Psychology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002695705,0.0001658947,0.0003609231,0.00008558334,0.00004126593,0.000007806308,0.0001946368,0.0001323506,0.00005056172],"category_scores_gemma":[0.0003450827,0.00013661,0.0001386577,0.000068323,0.0003547221,0.0000149618,0.00009832567,0.0001705518,0.000008468173],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000004847288,"about_ca_system_score_gemma":0.000060972,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000001598684,"about_ca_topic_score_gemma":2.937425e-7,"domain_scores_codex":[0.9982111,0.00046381,0.0007388546,0.0002741637,0.0001255442,0.0001865452],"domain_scores_gemma":[0.9985583,0.00003761302,0.0007306462,0.000257235,0.0002824687,0.0001337583],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.000470064,0.0002355958,0.01830622,0.0001048105,0.00001140267,0.00009752777,0.00002054706,0.000001564259,0.9787883,0.00006230476,0.0009807777,0.0009209185],"study_design_scores_gemma":[0.003081064,0.0129072,0.7577416,0.0001875983,0.0001072173,0.00816696,0.0001440638,0.00007022823,0.2147113,0.0002289012,0.002291365,0.0003624931],"study_design_candidate":"bench_or_experimental","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9897329,0.008290786,0.00007153876,0.001213295,0.0002704933,0.0002644863,0.000004773065,0.000006133926,0.0001456571],"genre_scores_gemma":[0.9908752,0.003191493,0.0005174507,0.005235847,0.0001163672,0.000006101754,0.00001095602,0.00001915312,0.00002745917],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.764077,"threshold_uncertainty_score":0.5570795,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.014887089046719,"score_gpt":0.2847054627214399,"score_spread":0.2698183736747209,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}