{"id":"W2337047219","doi":"10.15844/pedneurbriefs-20-11-7","title":"Juvenile GM2 Gangliosidoses","year":2006,"lang":"en","type":"article","venue":"Pediatric Neurology Briefs","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Gangliosidosis; Juvenile; Psychiatry; Pediatrics; Medicine; Psychology; Biology; Internal medicine; Disease; Ecology","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.000145932,0.0001743169,0.0003155346,0.0002820718,0.0001067394,0.00001762522,0.0001653446,0.0001795586,0.0005703901],"category_scores_gemma":[0.000223682,0.0001644989,0.0001221459,0.0006147333,0.0001164934,0.00006596785,0.00009994122,0.0004450849,0.0005961723],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00002118169,"about_ca_system_score_gemma":0.000150624,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0004312824,"about_ca_topic_score_gemma":0.00004291976,"domain_scores_codex":[0.9982483,0.00008653999,0.0002940166,0.0004333305,0.0003717421,0.0005661169],"domain_scores_gemma":[0.9991446,0.0001653137,0.00007196943,0.0003609658,0.0001071625,0.0001500121],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0003506893,0.0004349522,0.8711004,0.00007911801,0.00001473535,0.001896523,0.00002705971,0.00001642328,0.0007411962,0.0003218545,0.1240359,0.0009812063],"study_design_scores_gemma":[0.003130322,0.001049471,0.9096934,0.000001830838,0.0001645422,0.0009330868,0.000005951633,0.0001142249,0.0007120139,0.001099595,0.08281775,0.0002778633],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9713579,0.001833521,0.00005208451,0.006078678,0.000272966,0.0003372389,0.000007513547,0.0002093418,0.0198507],"genre_scores_gemma":[0.9923097,0.0001334613,0.00008499293,0.003114105,0.001714673,0.00003608811,0.00002800431,0.00004487229,0.002534084],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.04121811,"threshold_uncertainty_score":0.7662787,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01077033366621305,"score_gpt":0.2586116902794431,"score_spread":0.24784135661323,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}