{"id":"W2337047219","doi":"10.15844/pedneurbriefs-20-11-7","title":"Juvenile GM2 Gangliosidoses","year":2006,"lang":"en","type":"article","venue":"Pediatric Neurology Briefs","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Gangliosidosis; Juvenile; Psychiatry; Pediatrics; Medicine; Psychology; Biology; Internal medicine; Disease; Ecology","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002770051,0.0004433972,0.0002282175,0.001845421,0.0006887144,0.0003320001,0.0002229523,0.0001976294,0.001162888],"category_scores_gemma":[0.001461118,0.0003180459,0.0001997415,0.001004133,0.0006732091,0.0002578131,0.0003663728,0.0001520235,0.0001563282],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00058022,"about_ca_system_score_gemma":0.0003685723,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003780325,"about_ca_topic_score_gemma":0.007860573,"domain_scores_codex":[0.9996612,0.00004809077,0.00005552766,0.00008013985,0.00008469025,0.00007029524],"domain_scores_gemma":[0.9992769,0.0001925859,0.0002607243,0.00006689813,0.00007404757,0.000128714],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"case_report","study_design_scores_codex":[0.0001787692,0.00008164516,0.8808337,0.00007266998,0.00005762814,0.0944827,0.002227464,0.0001090502,0.0121973,0.0001949483,0.0002448043,0.009319454],"study_design_scores_gemma":[0.00002178201,0.0001387128,0.7149044,0.00002754898,0.00007537153,0.2797303,0.0008134448,0.000156407,0.002385183,0.0001153751,0.00161605,0.00001542442],"study_design_candidate":"case_report","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.99927,0.0002186152,0.00007529731,0.0000104563,0.000001661196,0.000006916431,0.00004617597,0.000003364799,0.0003674874],"genre_scores_gemma":[0.9993365,0.0002162815,0.0001431811,0.00001277039,0.000006388592,0.000006205609,0.0001120541,0.000002501229,0.0001640338],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003780325,"threshold_uncertainty_score":0.007516682,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01077033366621305,"score_gpt":0.2586116902794431,"score_spread":0.24784135661323,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}