{"id":"W2345099962","doi":"10.1186/s12883-016-0578-3","title":"CNS vasculitis and stroke as a complication of DOCK8 deficiency: a case report","year":2016,"lang":"en","type":"article","venue":"BMC Neurology","topic":"Immunodeficiency and Autoimmune Disorders","field":"Immunology and Microbiology","cited_by":29,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"University of Dammam; University of Calgary","keywords":"Medicine; Vasculitis; Cerebral vasculitis; Stroke (engine); Immunodeficiency; Neurology; Primary immunodeficiency; Optic neuritis; Immunology; Pediatrics; Dermatology; Disease; Pathology; Multiple sclerosis; Immune system","routes":{"ca_aff":false,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004977109,0.003224371,0.00220555,0.003566409,0.003785064,0.002900707,0.001809513,0.00619634,0.00232724],"category_scores_gemma":[0.002428362,0.001912143,0.001630292,0.0027099,0.002094415,0.002553036,0.003232294,0.004154277,0.001078301],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001591952,"about_ca_system_score_gemma":0.001168508,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002424271,"about_ca_topic_score_gemma":0.002775975,"domain_scores_codex":[0.9988795,0.0001119473,0.0001367934,0.0002649324,0.0001648732,0.0004418903],"domain_scores_gemma":[0.9982992,0.0003438123,0.0004129244,0.0001533789,0.0001012288,0.0006893757],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.00001065595,0.00002413339,0.002150742,0.00001817191,0.000008106268,0.9969566,0.00008789587,0.00002097031,0.0001560823,0.00005036233,0.0001229129,0.0003932843],"study_design_scores_gemma":[0.000006275049,0.0000224374,0.001392409,0.000007886423,0.000009081503,0.9981357,0.00006855866,0.00006365772,0.00006727662,0.00005999585,0.0001611457,0.000005513639],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9658592,0.0150878,0.004301277,0.002905888,0.0006599617,0.0002796,0.0003245218,0.0002622524,0.01031948],"genre_scores_gemma":[0.9913367,0.003877889,0.001380632,0.0007905195,0.001230399,0.00004588545,0.0001317653,0.0000265515,0.001179548],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.00619634,"threshold_uncertainty_score":0.01155049,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01266660623315708,"score_gpt":0.2366877083197771,"score_spread":0.22402110208662,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}