{"id":"W2412455279","doi":"10.1136/bcr-2016-215491","title":"Treatment of severe, refractory and rapidly evolving thrombotic thrombocytopenic purpura","year":2016,"lang":"en","type":"article","venue":"BMJ Case Reports","topic":"Complement system in diseases","field":"Immunology and Microbiology","cited_by":30,"is_retracted":false,"has_abstract":true,"ca_institutions":"London Health Sciences Centre","funders":"","keywords":"Medicine; Thrombotic thrombocytopenic purpura; Rituximab; Bortezomib; Splenectomy; Refractory (planetary science); Surgery; Cyclophosphamide; Pediatrics; Internal medicine; Platelet; Multiple myeloma; Chemotherapy; Lymphoma","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002754085,0.0006989404,0.0008160329,0.0006008942,0.001072539,0.0005119116,0.000502983,0.002223047,0.0008881671],"category_scores_gemma":[0.001629326,0.0002333767,0.0006837666,0.0004662114,0.0004933216,0.0005657722,0.0004570521,0.002085631,0.0005039748],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003329085,"about_ca_system_score_gemma":0.0002879523,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0003525893,"about_ca_topic_score_gemma":0.0008789549,"domain_scores_codex":[0.9997953,0.0000631904,0.00002528917,0.00002079534,0.00003678532,0.00005867881],"domain_scores_gemma":[0.9995932,0.0001021885,0.00006875864,0.00002363103,0.00002080415,0.0001913373],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0009450004,0.0004950147,0.01292094,0.0004745531,0.00008679398,0.911648,0.0005763646,0.0005105961,0.005911008,0.0004262809,0.005438034,0.0605675],"study_design_scores_gemma":[0.0004935567,0.003167864,0.02463773,0.0002776225,0.0000742065,0.9445055,0.000358933,0.001009646,0.002370571,0.001062005,0.02200174,0.00004071031],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.8950943,0.0648673,0.004071169,0.01412974,0.001443675,0.0003736733,0.0001352393,0.0002928015,0.01959215],"genre_scores_gemma":[0.9798265,0.01233212,0.0008826304,0.003095131,0.001809415,0.00005091422,0.000123501,0.00001607177,0.001863695],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002223047,"threshold_uncertainty_score":0.002971232,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0313673847896445,"score_gpt":0.3034175999408136,"score_spread":0.2720502151511691,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}