{"id":"W2508233820","doi":"10.1111/pde.12971","title":"Cutaneous Manifestations of Mucopolysaccharidoses","year":2016,"lang":"en","type":"review","venue":"Pediatric Dermatology","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":18,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of British Columbia","funders":"","keywords":"Medicine; Mucopolysaccharidosis; Lysosomal storage disorders; Hunter syndrome; Disease; Mucopolysaccharidosis I; Enzyme replacement therapy; Dermatology; Lysosomal storage disease; Pathology; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002403471,0.000910334,0.000796059,0.001870832,0.0003441861,0.0008236106,0.0003850738,0.0006870555,0.005458992],"category_scores_gemma":[0.0006003836,0.0001988345,0.0004650583,0.001155393,0.0003999326,0.0006932149,0.0005306157,0.0008671688,0.001363561],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003654938,"about_ca_system_score_gemma":0.0004171092,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0008515948,"about_ca_topic_score_gemma":0.001296349,"domain_scores_codex":[0.9997967,0.00003900226,0.00002933093,0.00004355625,0.0000562429,0.00003520074],"domain_scores_gemma":[0.9997647,0.00009313322,0.00005574354,0.00001258951,0.00004409668,0.00002970608],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00012806,0.00009248671,0.00233749,0.01711975,0.0002345359,0.01725796,0.0003317979,0.0003386309,0.0074688,0.003522956,0.04997063,0.9011968],"study_design_scores_gemma":[0.00006716503,0.0001302002,0.009778325,0.008232495,0.0002755009,0.2653778,0.0004053932,0.0001430926,0.002769533,0.001972738,0.7108021,0.00004571364],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.00331686,0.9848241,0.0004191903,0.0004230231,0.000253866,0.00002471632,0.0000968406,0.00004841487,0.01059282],"genre_scores_gemma":[0.047528,0.9449973,0.0005632062,0.0009358836,0.0004779639,0.00002086199,0.0001956439,0.00001005543,0.00527107],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.005458992,"threshold_uncertainty_score":0.01826209,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04267158470861299,"score_gpt":0.3706619183557363,"score_spread":0.3279903336471233,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}