{"id":"W2516987147","doi":"10.1016/j.rmed.2016.08.015","title":"Primary ciliary dyskinesia in Israel: Prevalence, clinical features, current diagnosis and management practices","year":2016,"lang":"en","type":"article","venue":"Respiratory Medicine","topic":"Cystic Fibrosis Research Advances","field":"Medicine","cited_by":12,"is_retracted":false,"has_abstract":false,"ca_institutions":"University of Alberta","funders":"European Respiratory Society","keywords":"Primary ciliary dyskinesia; Medicine; Bronchiectasis; Pediatrics; Kartagener Syndrome; Population; Consanguinity; Internal medicine; Pathology; Lung","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003749082,0.000172805,0.0002579243,0.001190463,0.0004137117,0.0006023113,0.0002653626,0.0004078152,0.001697712],"category_scores_gemma":[0.0008090845,0.0002107815,0.0002388956,0.001208025,0.0002912948,0.0005230914,0.0003477477,0.0003028917,0.0002327811],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0008110363,"about_ca_system_score_gemma":0.0007533751,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.02139723,"about_ca_topic_score_gemma":0.01796214,"domain_scores_codex":[0.9996805,0.00005692813,0.00005567865,0.00006312238,0.00006215236,0.00008158655],"domain_scores_gemma":[0.9995303,0.00009269037,0.0001606681,0.000008725255,0.0001073941,0.0001003653],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00003396335,0.00003742822,0.9963458,0.00001503623,0.00001450202,0.0001184502,0.0001942209,0.00001404674,0.0001165932,0.00001941227,0.0001867589,0.002903787],"study_design_scores_gemma":[0.000004177127,0.00003505369,0.997775,0.00002715273,0.00001123288,0.000700093,0.001097668,0.0000764717,0.00002392146,0.00002031399,0.0002249816,0.000003945271],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9964374,0.00160643,0.00003427959,0.000259251,0.000010075,0.000006151169,0.0004596908,0.000003751463,0.0011828],"genre_scores_gemma":[0.9979177,0.001133293,0.00005407442,0.0001080499,0.00002317666,0.000006497051,0.0005005096,0.000001770148,0.0002549108],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.02139723,"threshold_uncertainty_score":0.04254538,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.08778627876505653,"score_gpt":0.4399109422308318,"score_spread":0.3521246634657753,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}