{"id":"W2528511825","doi":"10.1002/art.39729","title":"Comparing Presenting Clinical Features in 48 Children With Microscopic Polyangiitis to 183 Children Who Have Granulomatosis With Polyangiitis (Wegener's): An ARChiVe Cohort Study","year":2016,"lang":"en","type":"article","venue":"Arthritis & Rheumatology","topic":"Vasculitis and related conditions","field":"Medicine","cited_by":146,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hospital for Sick Children; Alberta Children's Hospital; Janeway Children's Health and Rehabilitation Centre; McGill University Health Centre; University of Calgary; Simon Fraser University; Izaak Walton Killam Health Centre; Montreal Children's Hospital; Dalhousie University; BC Children's Hospital","funders":"Canadian Institutes of Health Research; Hospital for Sick Children; Dalhousie University; IWK Health Centre; Arthritis Society; Childhood Arthritis and Rheumatology Research Alliance; Texas Children's Hospital; McGill University; McGill University Health Centre; Children's Mercy Hospital; Child and Family Research Institute; Seattle Children's Research Institute; University of Louisville; Vasculitis Foundation; BC Children's Hospital; Cleveland Clinic; Vanderbilt University","keywords":"Granulomatosis with polyangiitis; Medicine; Microscopic polyangiitis; Wegener granulomatosis; Dermatology; Cohort; Pathology; Vasculitis; Pediatrics; Disease","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow"],"consensus_categories":[],"category_scores_codex":[0.0003521483,0.0004839398,0.001514832,0.0004995291,0.0003359318,0.00007727862,0.0003191999,0.0002594711,0.000120435],"category_scores_gemma":[0.00008252662,0.0003363324,0.0001744206,0.000374805,0.0005163384,0.0002359875,0.0001747228,0.0005785021,0.00008330415],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000059227,"about_ca_system_score_gemma":0.0001583119,"about_ca_topic_candidate":true,"about_ca_topic_consensus":true,"about_ca_topic_score_codex":0.007065429,"about_ca_topic_score_gemma":0.03296991,"domain_scores_codex":[0.9959684,0.0004537713,0.0009674949,0.001187936,0.0004195151,0.001002865],"domain_scores_gemma":[0.9980643,0.000166471,0.000234786,0.000857174,0.0001159511,0.0005613177],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.000203414,0.0008251375,0.988874,0.000009394586,0.001042506,0.0003204308,0.0009255153,0.000005698361,0.00006501488,0.0003201042,0.001356148,0.006052695],"study_design_scores_gemma":[0.01205354,0.001770389,0.9746232,0.001549295,0.0002090468,0.008623241,0.0003324909,0.000008116706,0.0002551084,0.00005883977,0.00003659414,0.0004801599],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9941356,0.001166188,0.0002309926,0.001007024,0.0001372942,0.002550928,0.0001578703,0.0001735063,0.0004406285],"genre_scores_gemma":[0.9965763,0.001258994,0.001051102,0.0002164343,0.0000791059,0.0002847839,0.0002694034,0.0001031421,0.0001607256],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.02590448,"threshold_uncertainty_score":0.9999089,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.008619610463009941,"score_gpt":0.2725509981013614,"score_spread":0.2639313876383514,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}