{"id":"W2548147209","doi":"10.1182/blood.v122.21.2360.2360","title":"Long-Term Outcomes Of a Small Cohort At a Single Canadian Centre Of Severe Subunit A FXIII Deficient Patients (F13A1: c.691-1G&gt;A) Treated Prophylactically With Fibrogammin P","year":2013,"lang":"en","type":"article","venue":"Blood","topic":"Hemophilia Treatment and Research","field":"Medicine","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"Memorial University of Newfoundland; St. John’s Health Sciences Centre","funders":"","keywords":"Medicine; Cohort; Factor XIII deficiency; Pediatrics; Hemarthrosis; Surgery; Factor XIII; Compound heterozygosity; Internal medicine; Allele","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003426603,0.0004184108,0.0005320571,0.000683128,0.002993163,0.001098793,0.0005771588,0.0005759834,0.001455368],"category_scores_gemma":[0.0007956506,0.0002732526,0.0007241592,0.00103819,0.0007380455,0.0004053125,0.0007239867,0.001095694,0.0003992027],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.004342856,"about_ca_system_score_gemma":0.004061956,"about_ca_topic_candidate":true,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.2804231,"about_ca_topic_score_gemma":0.3463032,"domain_scores_codex":[0.9994869,0.00003046792,0.00003018973,0.0001047163,0.0001350786,0.0002126556],"domain_scores_gemma":[0.9985452,0.00008073903,0.0002349415,0.00006950859,0.0003042474,0.0007653412],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0004061174,0.0003350484,0.98745,0.00001821019,0.0001366246,0.00272283,0.0005514785,0.0001120747,0.001225836,0.00005186689,0.0008878836,0.006102026],"study_design_scores_gemma":[0.00004478481,0.001064304,0.9931731,0.00002673685,0.0001142135,0.003280549,0.001032052,0.0002143574,0.0002018732,0.00003287365,0.0007835174,0.00003158283],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9986332,0.0001894969,0.00006794684,0.0001088374,0.000009049027,0.00003047762,0.0003480335,0.000003576471,0.0006094408],"genre_scores_gemma":[0.9981439,0.0002390147,0.0001014537,0.0001047778,0.00002957308,0.00002067104,0.000914351,0.000003793597,0.0004423714],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.719577,"threshold_uncertainty_score":0.5575817,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01818853324978805,"score_gpt":0.2300581144179548,"score_spread":0.2118695811681668,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}