{"id":"W2561150920","doi":"10.1182/blood.v110.11.2088.2088","title":"Clinical and Outcomes Findings for Thrombotic Thrombocytopenic Purpura among 467 Persons with Severely Versus Not Severely Deficient ADAMTS-13 Levels.","year":2007,"lang":"en","type":"article","venue":"Blood","topic":"Complement system in diseases","field":"Immunology and Microbiology","cited_by":4,"is_retracted":false,"has_abstract":true,"ca_institutions":"Canadian Apheresis Group","funders":"","keywords":"ADAMTS13; Thrombotic thrombocytopenic purpura; Medicine; Thrombotic microangiopathy; Microangiopathic hemolytic anemia; Internal medicine; Gastroenterology; Pediatrics; Platelet; Disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003169544,0.0002619697,0.0002818462,0.0009877557,0.000568188,0.0004826459,0.0002324212,0.0004120712,0.001822489],"category_scores_gemma":[0.001246981,0.000279104,0.0003714437,0.0008861979,0.0002793632,0.0004188374,0.0003575785,0.0004082517,0.0002969868],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005304501,"about_ca_system_score_gemma":0.0002991999,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.007139324,"about_ca_topic_score_gemma":0.005963355,"domain_scores_codex":[0.9996358,0.00006520131,0.00004940736,0.0001067316,0.00006545038,0.00007730613],"domain_scores_gemma":[0.9991916,0.0001037359,0.0003744662,0.00003836234,0.00009666059,0.0001950541],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0000499399,0.00001829809,0.9991911,0.00000434011,0.0000153238,0.0001628991,0.00004168613,0.00001723973,0.0000587123,0.000005548639,0.00008149684,0.0003534041],"study_design_scores_gemma":[0.000007936913,0.00007151919,0.9986963,0.000003857165,0.00001347902,0.0008086203,0.0001810089,0.00007409473,0.00003973842,0.000009817402,0.0000910551,0.000002604585],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9988303,0.0001166335,0.00003201859,0.00001758117,0.00000388937,0.000009221906,0.0006938209,0.000002317184,0.0002942177],"genre_scores_gemma":[0.9991605,0.00005361285,0.00002325051,0.0000116703,0.000006684898,0.00001158082,0.0006294982,9.803011e-7,0.0001021636],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.007139324,"threshold_uncertainty_score":0.01419556,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.06099010723279662,"score_gpt":0.3243219378792406,"score_spread":0.2633318306464439,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}