{"id":"W2561150920","doi":"10.1182/blood.v110.11.2088.2088","title":"Clinical and Outcomes Findings for Thrombotic Thrombocytopenic Purpura among 467 Persons with Severely Versus Not Severely Deficient ADAMTS-13 Levels.","year":2007,"lang":"en","type":"article","venue":"Blood","topic":"Complement system in diseases","field":"Immunology and Microbiology","cited_by":4,"is_retracted":false,"has_abstract":true,"ca_institutions":"Canadian Apheresis Group","funders":"","keywords":"ADAMTS13; Thrombotic thrombocytopenic purpura; Medicine; Thrombotic microangiopathy; Microangiopathic hemolytic anemia; Internal medicine; Gastroenterology; Pediatrics; Platelet; Disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow"],"consensus_categories":[],"category_scores_codex":[0.0007519592,0.0003663231,0.0007154194,0.0001181446,0.0004060443,0.00005093981,0.0003532055,0.0002625647,0.0003483501],"category_scores_gemma":[0.0002597322,0.0002929225,0.0002350638,0.0001392518,0.0005255424,0.0001463658,0.0001922774,0.0002847941,0.000120784],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00004595381,"about_ca_system_score_gemma":0.0001296923,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00008247323,"about_ca_topic_score_gemma":0.0005974544,"domain_scores_codex":[0.997659,0.0001234984,0.0006594447,0.000689882,0.0001185659,0.0007495821],"domain_scores_gemma":[0.9977576,0.001359207,0.0002147358,0.0004683349,0.0001019615,0.00009818536],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001753862,0.0009946257,0.9900241,0.00009551578,0.001573688,0.00002407081,0.000469539,0.000002670233,0.001292649,0.0009433234,0.002462094,0.0003638967],"study_design_scores_gemma":[0.01603074,0.001261186,0.9772791,0.00007797514,0.0008400726,0.00006667834,0.0008158408,0.00000268341,0.001770681,0.00002076147,0.001410078,0.0004241525],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9957993,0.0006925702,0.0002640737,0.0001750595,0.0008911105,0.001175979,0.0002742996,0.0001287622,0.0005988601],"genre_scores_gemma":[0.9982636,0.00001062819,0.000502797,0.0001858173,0.00004650485,0.00006189589,0.00007140396,0.00004493725,0.000812394],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01427688,"threshold_uncertainty_score":0.9999523,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.06099010723279662,"score_gpt":0.3243219378792406,"score_spread":0.2633318306464439,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}