{"id":"W2589792316","doi":"10.1182/blood.v118.21.3303.3303","title":"Eculizumab Is An Effective Long-Term Treatment In Patients with Atypical Hemolytic Uremic Syndrome (aHUS) Previously Receiving Chronic Plasma Exchange/Infusion (PE/PI): Extension Study Results,","year":2011,"lang":"en","type":"article","venue":"Blood","topic":"Complement system in diseases","field":"Immunology and Microbiology","cited_by":7,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hospital for Sick Children","funders":"","keywords":"Medicine; Eculizumab; Atypical hemolytic uremic syndrome; Thrombotic microangiopathy; Dialysis; Clinical endpoint; Internal medicine; Surrogate endpoint; Regimen; Renal function; Gastroenterology; Surgery; Randomized controlled trial; Immunology; Complement system; Antibody","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow"],"consensus_categories":[],"category_scores_codex":[0.0002395105,0.0004344231,0.0005970949,0.0002200844,0.0001895401,0.00001836744,0.0002932267,0.0001879673,0.0004235909],"category_scores_gemma":[0.00005219719,0.0003337759,0.00009057527,0.000202454,0.0000931275,0.0001660441,0.0001851808,0.0001998797,0.0002023934],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004415592,"about_ca_system_score_gemma":0.00008780051,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000341312,"about_ca_topic_score_gemma":0.001258983,"domain_scores_codex":[0.9971271,0.0006895348,0.0005513505,0.0009040879,0.0001224661,0.0006054632],"domain_scores_gemma":[0.9985872,0.0001292677,0.0002553115,0.0008610565,0.00008823995,0.00007891558],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.005049563,0.01458952,0.9645451,0.0001092942,0.0005518371,0.000274988,0.006061329,0.000001479397,0.001120804,0.000001384284,0.00006217002,0.007632562],"study_design_scores_gemma":[0.03243938,0.01857078,0.9443414,0.000677795,0.0004755267,0.0001272776,0.0001576399,0.000002480265,0.002830114,0.000003720454,0.00001275929,0.000361128],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9939254,0.0009246501,0.000002687372,0.000006756494,0.0002267992,0.004656329,0.00007935973,0.0001198568,0.0000581926],"genre_scores_gemma":[0.9989886,0.00003129676,0.00002118852,0.00001419243,0.00002370344,0.0004328521,0.0003196609,0.00004540539,0.0001230959],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.02738982,"threshold_uncertainty_score":0.9999114,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01860261064052004,"score_gpt":0.242432139954303,"score_spread":0.223829529313783,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}