{"id":"W2591186241","doi":"10.1182/blood.v106.11.3978.3978","title":"Clinical and Laboratory Control of a Man with Chronic Recurrent Thrombotic Thrombocytopenic Purpura (TTP) Since Birth, with Bi-Weekly Infusion of Plasma.","year":2005,"lang":"en","type":"article","venue":"Blood","topic":"Complement system in diseases","field":"Immunology and Microbiology","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"St. Boniface Hospital","funders":"","keywords":"Medicine; Thrombotic thrombocytopenic purpura; Prednisone; Schistocyte; Internal medicine; Jaundice; Splenectomy; Pediatrics; Gastroenterology; Hemolytic anemia; Dipyridamole; Microangiopathic hemolytic anemia; Surgery; Platelet","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004015999,0.0007139198,0.0003920805,0.0008636119,0.0008539337,0.0003458889,0.0003352625,0.001213768,0.001129581],"category_scores_gemma":[0.002123851,0.000281886,0.0003456659,0.000469275,0.000609797,0.0003435649,0.0002875704,0.001294404,0.0002758763],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006537218,"about_ca_system_score_gemma":0.0004259106,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003948678,"about_ca_topic_score_gemma":0.004945338,"domain_scores_codex":[0.9995789,0.00008562448,0.00004201656,0.0001166436,0.00008868343,0.00008815146],"domain_scores_gemma":[0.9989377,0.0001821187,0.0001713355,0.00005551616,0.0001278739,0.0005254748],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0008187926,0.0005268529,0.3041059,0.0001109044,0.00009523443,0.6678558,0.001434489,0.0004226274,0.009259296,0.0003439456,0.002428637,0.01259749],"study_design_scores_gemma":[0.00007898306,0.002520966,0.4822051,0.00004510012,0.00006533267,0.5082785,0.0003278842,0.0006082214,0.002166029,0.0001378404,0.003519525,0.00004652905],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9862917,0.001958251,0.0008098874,0.00111537,0.0001414263,0.00007101884,0.0002767221,0.000101163,0.00923442],"genre_scores_gemma":[0.9978958,0.0002829406,0.000290354,0.0003190989,0.0000859319,0.00001342308,0.0001347567,0.000008884303,0.000968762],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003948678,"threshold_uncertainty_score":0.007851422,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01240917667800485,"score_gpt":0.2590720886435195,"score_spread":0.2466629119655147,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}