{"id":"W2729453381","doi":"10.1111/ene.13349","title":"Clinical characterization of dystonia in adult patients with Huntington's disease","year":2017,"lang":"en","type":"article","venue":"European Journal of Neurology","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":37,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"Seventh Framework Programme; Medical Research Council; Ipsen; Hersenstichting; Medtronic; Allergan; Academy of Medical Sciences; Stichting Vrienden Beatrix Kinderziekenhuis; Prinses Beatrix Spierfonds; Fonds Psychische Gezondheid; Fonds NutsOhra; Ipsen Fund; European Commission","keywords":"Dystonia; Huntington's disease; Rating scale; Chorea; Medicine; Spasmodic Torticollis; Movement disorders; Physical therapy; Severity of illness; Neurological disorder; Disease; Physical medicine and rehabilitation; Psychology; Central nervous system disease; Internal medicine; Psychiatry","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003380413,0.0001389066,0.0002850294,0.0001377739,0.0001027011,0.00004177793,0.0006905836,0.00001746941,0.00001753941],"category_scores_gemma":[0.002912648,0.0001100454,0.00008907625,0.00006661028,0.0003596821,0.000223137,0.0001392312,0.0002940859,0.00001380256],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000003723186,"about_ca_system_score_gemma":0.00006596433,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":4.881077e-7,"about_ca_topic_score_gemma":0.000001089196,"domain_scores_codex":[0.9969119,0.001588517,0.0007234091,0.0002967776,0.0002839028,0.0001954733],"domain_scores_gemma":[0.9974554,0.000121023,0.001534187,0.0004468487,0.0002571864,0.0001853122],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00126068,0.0004366538,0.9179938,0.00001112242,0.000004147452,0.0003821468,0.00003672698,0.00004650655,0.07725651,0.00005337909,0.00001850263,0.002499798],"study_design_scores_gemma":[0.00205378,0.00128119,0.9834362,0.00002634705,0.00001812964,0.000007352706,7.416974e-7,0.00003425267,0.0127581,0.000009252743,0.0002894173,0.00008520168],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9981992,0.000001712643,0.0000710535,0.0007335214,0.000537376,0.0001255335,0.00001997532,0.000005599191,0.0003060135],"genre_scores_gemma":[0.9984076,0.00003107201,0.00004743601,0.001322235,0.0001357677,5.867964e-7,0.000001622266,0.000032044,0.00002162653],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.06544241,"threshold_uncertainty_score":0.4487521,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02396863976060783,"score_gpt":0.277841084526532,"score_spread":0.2538724447659242,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}