{"id":"W2729453381","doi":"10.1111/ene.13349","title":"Clinical characterization of dystonia in adult patients with Huntington's disease","year":2017,"lang":"en","type":"article","venue":"European Journal of Neurology","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":37,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"Seventh Framework Programme; Medical Research Council; Ipsen; Hersenstichting; Medtronic; Allergan; Academy of Medical Sciences; Stichting Vrienden Beatrix Kinderziekenhuis; Prinses Beatrix Spierfonds; Fonds Psychische Gezondheid; Fonds NutsOhra; Ipsen Fund; European Commission","keywords":"Dystonia; Huntington's disease; Rating scale; Chorea; Medicine; Spasmodic Torticollis; Movement disorders; Physical therapy; Severity of illness; Neurological disorder; Disease; Physical medicine and rehabilitation; Psychology; Central nervous system disease; Internal medicine; Psychiatry","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003124067,0.0002643197,0.0003653778,0.0006399037,0.0002539062,0.0003130689,0.000149798,0.0004416161,0.001415291],"category_scores_gemma":[0.00151454,0.0001014612,0.0001180508,0.0004046419,0.0003033919,0.000234734,0.0002528843,0.0001883984,0.0002565905],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001767812,"about_ca_system_score_gemma":0.0001387848,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001023494,"about_ca_topic_score_gemma":0.001968372,"domain_scores_codex":[0.9998104,0.00004076989,0.00004397791,0.0000392088,0.00003795539,0.00002780819],"domain_scores_gemma":[0.999162,0.0002354094,0.0003194514,0.00001886816,0.00009994076,0.0001643351],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0004477626,0.00003624381,0.9892858,0.00003746299,0.00001924782,0.002362411,0.0002219389,0.00005454784,0.003402261,0.00001301273,0.0001872367,0.003932097],"study_design_scores_gemma":[0.000008121357,0.0001636123,0.99494,0.000005946133,0.000005796427,0.004588661,0.00008600827,0.00004298361,0.00006580209,0.000006780834,0.00008425186,0.000002133228],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9987445,0.0004351147,0.00005991143,0.00002236895,0.000003320865,0.00001450114,0.0001229,0.000003781127,0.0005936115],"genre_scores_gemma":[0.9993944,0.0001179655,0.00009800679,0.00003219447,0.000008848093,0.00001079761,0.0002369098,7.410092e-7,0.0001001978],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001415291,"threshold_uncertainty_score":0.004734576,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02396863976060783,"score_gpt":0.277841084526532,"score_spread":0.2538724447659242,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}