{"id":"W2751582300","doi":"10.1159/000479859","title":"Significant Improvement of Clinical Symptoms, Bone Lesions, and Bone Turnover after Long-Term Zoledronic Acid Treatment in Patients with a Severe Form of Camurati-Engelmann Disease","year":2017,"lang":"en","type":"article","venue":"Molecular Syndromology","topic":"Dermatological and Skeletal Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":13,"is_retracted":false,"has_abstract":true,"ca_institutions":"Pediatric Oncology Group","funders":"","keywords":"Zoledronic acid; Medicine; Bone remodeling; N-terminal telopeptide; Internal medicine; Bisphosphonate; Proband; Bone pain; Osteocalcin; Medullary cavity; Endocrinology; Gastroenterology; Osteoporosis; Alkaline phosphatase","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001069358,0.000247837,0.0005564347,0.00004952077,0.00004967721,0.00001233649,0.0001781707,0.0002034399,0.00001698279],"category_scores_gemma":[0.00007267732,0.0001797311,0.0001584862,0.00002994748,0.0004162668,0.00001052102,0.000213231,0.00009640951,0.000001837846],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00001642389,"about_ca_system_score_gemma":0.00009093704,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00003111189,"about_ca_topic_score_gemma":0.000122049,"domain_scores_codex":[0.9984182,0.00008977756,0.0005659082,0.0004781345,0.0001488788,0.0002990744],"domain_scores_gemma":[0.9987673,0.00001128343,0.0003349774,0.0006619103,0.00006795697,0.0001565842],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001557248,0.001458202,0.9748656,0.0001531842,0.0002262238,0.001471445,0.00002337146,0.000003149511,0.009141911,0.00004794608,0.000008355235,0.01104342],"study_design_scores_gemma":[0.004250648,0.003102439,0.9875244,0.00005708864,0.0001015588,0.0000840744,0.000004272552,0.000005960599,0.004481645,0.0001022027,0.00004523385,0.0002404311],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9975893,0.001469576,0.0001059952,0.00009104676,0.00005262823,0.000563681,0.00007014949,0.000003936128,0.00005363988],"genre_scores_gemma":[0.9993974,0.0001452441,0.00006399839,0.00008430143,0.000007475641,0.00008770473,0.0001298539,0.00001932553,0.00006472519],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.0126589,"threshold_uncertainty_score":0.7329221,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.007902839376336198,"score_gpt":0.2578431271159104,"score_spread":0.2499402877395742,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}