{"id":"W2755141428","doi":"10.1016/j.jaip.2017.06.041","title":"Autosomal Dominant Hyper-IgE Syndrome in the USIDNET Registry","year":2017,"lang":"en","type":"article","venue":"The Journal of Allergy and Clinical Immunology In Practice","topic":"Immunodeficiency and Autoimmune Disorders","field":"Immunology and Microbiology","cited_by":98,"is_retracted":false,"has_abstract":false,"ca_institutions":"Centre Hospitalier Universitaire Sainte-Justine","funders":"National Institutes of Health; Hort Innovation; National Institute of Allergy and Infectious Diseases; US Immunodeficiency Network","keywords":"Medicine; Exact test; Eosinophilia; Internal medicine; Immunoglobulin E; Dermatology; Pediatrics; Immunology; Gastroenterology; Antibody","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["research_integrity"],"consensus_categories":[],"category_scores_codex":[0.006465181,0.0002041063,0.0005305603,0.00009320897,0.0007195421,0.00005880883,0.001834098,0.0004864977,0.00007132247],"category_scores_gemma":[0.004504222,0.0001146662,0.0001552746,0.00009520094,0.001991017,0.0005882527,0.0002822071,0.002714958,0.0000630194],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00002106386,"about_ca_system_score_gemma":0.0001657761,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0004931683,"about_ca_topic_score_gemma":0.0000948672,"domain_scores_codex":[0.9955719,0.002487455,0.001239919,0.0001951077,0.00008000145,0.0004256838],"domain_scores_gemma":[0.9936526,0.003749602,0.001583661,0.0009032878,0.0001022692,0.000008604413],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"observational","study_design_scores_codex":[0.1107182,0.03665399,0.08021638,0.0001024313,0.04874959,0.01245815,0.06081633,0.0004339564,0.1235947,0.1060495,0.006947108,0.4132597],"study_design_scores_gemma":[0.007599951,0.001826323,0.8239424,0.0001851171,0.0005001597,0.01782268,0.01511732,0.00001014576,0.0002121852,0.001553028,0.1309319,0.0002987444],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9306159,0.04744569,0.00001292131,0.01695763,0.001673599,0.0001408705,0.000001814294,0.000004816766,0.003146733],"genre_scores_gemma":[0.9732928,0.02522704,0.00002330151,0.0009808528,0.00001393374,0.000003708316,0.000002104623,0.00001032275,0.0004459116],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.7437261,"threshold_uncertainty_score":0.9995858,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02504110518389318,"score_gpt":0.3300660156309435,"score_spread":0.3050249104470503,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}