{"id":"W2795584931","doi":"10.1542/peds.2016-3896","title":"Successful Liver Transplants for Liver Failure Associated With Pyruvate Kinase Deficiency","year":2018,"lang":"en","type":"article","venue":"PEDIATRICS","topic":"Erythrocyte Function and Pathophysiology","field":"Medicine","cited_by":17,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; Montreal Children's Hospital; Université de Montréal; Centre Hospitalier Universitaire Sainte-Justine","funders":"","keywords":"Medicine; Pyruvate kinase deficiency; Splenectomy; Hemolysis; Neonatal cholestasis; Unconjugated hyperbilirubinemia; Liver transplantation; Hemolytic anemia; Liver function tests; Anemia; Internal medicine; Liver failure; Cholestasis; Liver function; Gastroenterology; Bilirubin; Pyruvate kinase; Transplantation; Spleen; Metabolism","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003599126,0.0008478755,0.0005243084,0.0007700664,0.001110181,0.0005182103,0.0004348651,0.0009861192,0.001099745],"category_scores_gemma":[0.001772113,0.0002324642,0.0005471459,0.000289432,0.0006704687,0.0004698827,0.0008474834,0.001188327,0.0005022807],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004644456,"about_ca_system_score_gemma":0.0005568874,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0003978367,"about_ca_topic_score_gemma":0.000799792,"domain_scores_codex":[0.9997048,0.00005137222,0.0000346425,0.00002830692,0.00005688501,0.0001240096],"domain_scores_gemma":[0.9992028,0.0001929039,0.0001480115,0.00007533448,0.00003939034,0.0003415485],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0003084272,0.0002730568,0.09405425,0.00009199004,0.00004956758,0.8718668,0.0004163942,0.0002733858,0.009977257,0.0004868327,0.001074157,0.02112792],"study_design_scores_gemma":[0.00005218978,0.0005095847,0.05811435,0.00004027894,0.0000425816,0.9323323,0.0001709205,0.0007032523,0.00549269,0.0002390732,0.002280655,0.00002213286],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.98456,0.004257267,0.00367092,0.0009450878,0.0002904357,0.00007046297,0.0000942771,0.0002761198,0.005835352],"genre_scores_gemma":[0.9974428,0.0008165971,0.0007379472,0.0002246702,0.0001488369,0.0000119162,0.00007396335,0.00002682543,0.0005163568],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001110181,"threshold_uncertainty_score":0.003678977,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01976498483090643,"score_gpt":0.2460041409536044,"score_spread":0.226239156122698,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}