{"id":"W2795584931","doi":"10.1542/peds.2016-3896","title":"Successful Liver Transplants for Liver Failure Associated With Pyruvate Kinase Deficiency","year":2018,"lang":"en","type":"article","venue":"PEDIATRICS","topic":"Erythrocyte Function and Pathophysiology","field":"Medicine","cited_by":17,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; Montreal Children's Hospital; Université de Montréal; Centre Hospitalier Universitaire Sainte-Justine","funders":"","keywords":"Medicine; Pyruvate kinase deficiency; Splenectomy; Hemolysis; Neonatal cholestasis; Unconjugated hyperbilirubinemia; Liver transplantation; Hemolytic anemia; Liver function tests; Anemia; Internal medicine; Liver failure; Cholestasis; Liver function; Gastroenterology; Bilirubin; Pyruvate kinase; Transplantation; Spleen; Metabolism","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001459802,0.000168893,0.0002517007,0.0001308571,0.0001617791,0.0000125973,0.00008321663,0.0001823147,0.0003077144],"category_scores_gemma":[0.0001622875,0.0001288794,0.00008368726,0.0004065201,0.0001159026,0.0000780403,0.0000131311,0.0001614676,0.000142179],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00004604235,"about_ca_system_score_gemma":0.0001341661,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00003193463,"about_ca_topic_score_gemma":0.0001827976,"domain_scores_codex":[0.9989167,0.00003363176,0.0001832641,0.0003062987,0.0002069389,0.000353108],"domain_scores_gemma":[0.9990099,0.0001781332,0.0001035298,0.0001871763,0.0003785526,0.0001426765],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0105478,0.004010201,0.7748426,0.003020603,0.0004041896,0.001297172,0.008756737,0.00003868651,0.02052154,0.002107288,0.1603455,0.0141077],"study_design_scores_gemma":[0.03997945,0.03032197,0.7651538,0.0004746818,0.006526341,0.000387137,0.001155839,0.008168727,0.01301215,0.0007360408,0.1308154,0.003268412],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9928448,0.0004003308,0.004382489,0.0002167607,0.0003584954,0.0004602101,0.0001082646,0.0001343351,0.001094357],"genre_scores_gemma":[0.9949393,0.0004170833,0.001393379,0.0008372807,0.001054807,0.00002769136,0.0001641658,0.00003216829,0.001134154],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.02953009,"threshold_uncertainty_score":0.5255551,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01976498483090643,"score_gpt":0.2460041409536044,"score_spread":0.226239156122698,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}