{"id":"W2795867865","doi":"10.1111/1756-185x.13283","title":"Diagnosis and management of <scp>ADA</scp>2 deficient polyarteritis nodosa","year":2018,"lang":"en","type":"review","venue":"International Journal of Rheumatic Diseases","topic":"Vasculitis and related conditions","field":"Medicine","cited_by":36,"is_retracted":false,"has_abstract":true,"ca_institutions":"Mount Sinai Hospital; BC Children's Hospital","funders":"","keywords":"Polyarteritis nodosa; Medicine; Hypogammaglobulinemia; Phenotype; Rash; Disease; Pathogenesis; Inflammation; Systemic inflammation; Dermatology; Immunology; Vasculitis; Gene; Pathology; Genetics; Biology; Antibody","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001422682,0.0002360371,0.001075338,0.0004528909,0.00003850152,0.00005885735,0.0002912826,0.0001009096,0.0002204214],"category_scores_gemma":[0.000190109,0.0001699677,0.0007789637,0.00013085,0.0001530366,0.00009659857,0.0001053978,0.0001714882,0.00002824454],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001071878,"about_ca_system_score_gemma":0.000170844,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000006945762,"about_ca_topic_score_gemma":4.564229e-7,"domain_scores_codex":[0.9976826,0.00006177051,0.001148071,0.0001688661,0.0007906015,0.0001481174],"domain_scores_gemma":[0.9978009,0.0002800415,0.001065284,0.0001817256,0.000444154,0.0002279332],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.000008012323,0.0007128383,0.0002828743,0.01527512,0.006956256,0.0006955542,0.00009894757,9.160158e-7,9.093141e-8,0.0008169069,0.01418091,0.9609716],"study_design_scores_gemma":[0.001649505,0.0003527456,0.003478119,0.2385431,0.008808098,0.003946117,0.000263921,0.00001057622,0.000001517018,0.0004209945,0.7424001,0.0001252463],"study_design_candidate":"design_other","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.002250696,0.9952777,0.00009288487,0.0001287817,0.0008981478,0.0003329145,0.0003544825,0.000009587829,0.0006548208],"genre_scores_gemma":[0.001821967,0.9970552,0.0005291898,0.00003621666,0.0001606119,0.00003677336,0.00009938555,0.00002855802,0.0002321319],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.9608463,"threshold_uncertainty_score":0.6931081,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0259552689788209,"score_gpt":0.3232233877403647,"score_spread":0.2972681187615438,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}