{"id":"W2800740578","doi":"10.2174/1871527317666180419115029","title":"Current and Promising Therapies in Autosomal Recessive Ataxias","year":2018,"lang":"en","type":"review","venue":"CNS & Neurological Disorders - Drug Targets","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":11,"is_retracted":false,"has_abstract":true,"ca_institutions":"Université Laval","funders":"Canadian Institutes of Health Research","keywords":"Ataxia; Ataxia-telangiectasia; Medicine; Disease; Cerebellar ataxia; Bioinformatics; Neuroscience; Genetics; Biology; Pathology; Psychiatry","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003424429,0.0007114679,0.0007374254,0.00189224,0.0002479467,0.0005965559,0.0005729959,0.0008402702,0.004013906],"category_scores_gemma":[0.0004119765,0.0001397669,0.0004508419,0.0009676039,0.0002602164,0.0007731539,0.000541781,0.001599425,0.001633082],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004217278,"about_ca_system_score_gemma":0.0005787682,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000636871,"about_ca_topic_score_gemma":0.001693665,"domain_scores_codex":[0.9998827,0.0000213789,0.00001991498,0.00001943858,0.00004177996,0.00001469862],"domain_scores_gemma":[0.9998566,0.00006027511,0.00002196946,0.000004650551,0.00004266001,0.00001387239],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00008518311,0.00008892089,0.0001427839,0.01204089,0.00006252525,0.0003740173,0.00006813199,0.0002666318,0.002470621,0.002679684,0.02388777,0.9578328],"study_design_scores_gemma":[0.00002683821,0.0001455802,0.000753649,0.005014892,0.0001393583,0.002886651,0.0000650874,0.000112512,0.0008475153,0.00222183,0.9877716,0.00001442054],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.0001819609,0.9979597,0.0001309993,0.0002844666,0.0001766096,0.000005029197,0.00001871302,0.000009848962,0.001232689],"genre_scores_gemma":[0.00117002,0.9972931,0.0002831804,0.0002631037,0.0001408493,0.000008307283,0.00004305812,0.000001955633,0.0007963804],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.004013906,"threshold_uncertainty_score":0.01342779,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.05530086348238081,"score_gpt":0.3284631310583688,"score_spread":0.2731622675759879,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}