{"id":"W2803426724","doi":"10.1093/ndt/gfy104.sp004","title":"SP004EFFECTS OF LONG-TERM MIGALASTAT TREATMENT ON RENAL FUNCTION BY BASELINE PROTEINURIA IN PATIENTS (PTS) WITH FABRY DISEASE","year":2018,"lang":"en","type":"article","venue":"Nephrology Dialysis Transplantation","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":5,"is_retracted":false,"has_abstract":true,"ca_institutions":"Université de Montréal; Hôpital du Sacré-Cœur de Montréal","funders":"Lomonosov Moscow State University; I.M. Sechenov First Moscow State Medical University","keywords":"Medicine; Proteinuria; Fabry disease; Renal function; Internal medicine; Term (time); Disease; Urology; Kidney","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001548207,0.0002112908,0.0003569612,0.0003155618,0.000055842,0.000007278266,0.00005820993,0.0001149448,0.0001939074],"category_scores_gemma":[0.00003122771,0.0001597501,0.00008565433,0.0003816532,0.000185776,0.00009880946,0.000004207855,0.000120835,0.00003701999],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000154611,"about_ca_system_score_gemma":0.00009665499,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0001506398,"about_ca_topic_score_gemma":0.000726024,"domain_scores_codex":[0.9982892,0.0002823056,0.0003052755,0.0004141344,0.0004233603,0.0002857693],"domain_scores_gemma":[0.9992226,0.0001049481,0.0001096952,0.0002457473,0.0001654184,0.0001515685],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.06301598,0.002833662,0.8819506,0.0002427588,0.000337665,0.0001355163,0.0005197074,0.0000580716,0.01578136,0.000006237382,0.00009494084,0.0350235],"study_design_scores_gemma":[0.01463031,0.01174719,0.9593429,0.0001362214,0.0007750125,0.000003489286,0.000006601383,0.0002517045,0.01291959,0.00000905502,0.00004247762,0.0001354875],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9951775,0.0000535942,0.002971481,0.0002169149,0.00003879959,0.001340995,0.00007478483,0.00003113083,0.00009476667],"genre_scores_gemma":[0.9974096,0.00008571265,0.00005510249,0.0002387071,0.00007795283,0.0001981049,0.001826212,0.00002607533,0.00008253545],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.07739227,"threshold_uncertainty_score":0.6514419,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.008713926975726713,"score_gpt":0.2570812092156321,"score_spread":0.2483672822399054,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}