{"id":"W2892628441","doi":"10.1016/j.jpeds.2018.08.061","title":"Health-Related Quality of Life in Children and Young Adults with Marfan Syndrome","year":2018,"lang":"en","type":"article","venue":"The Journal of Pediatrics","topic":"Connective tissue disorders research","field":"Biochemistry, Genetics and Molecular Biology","cited_by":48,"is_retracted":false,"has_abstract":false,"ca_institutions":"SickKids Foundation; Hospital for Sick Children; University of Toronto","funders":"National Heart, Lung, and Blood Institute; Marfan Foundation","keywords":"Medicine; Marfan syndrome; Pediatrics; Quality of life (healthcare); Young adult; Gerontology; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001223746,0.00006722753,0.0001923487,0.00008209219,0.00003776841,0.000004737816,0.0001665781,0.00005324003,0.000007208527],"category_scores_gemma":[0.0003489822,0.00004478737,0.00002506707,0.0002004527,0.0001298122,0.000004135916,0.00006613908,0.0001552185,7.776973e-7],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00001174823,"about_ca_system_score_gemma":0.0001837121,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0007962387,"about_ca_topic_score_gemma":0.0006668477,"domain_scores_codex":[0.9989682,0.0002424781,0.000366966,0.00008128415,0.000199227,0.0001418217],"domain_scores_gemma":[0.9991851,0.00003753927,0.0003472879,0.000139152,0.0002162178,0.00007468009],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00144635,0.00008172578,0.9947699,0.00005635226,0.00003326891,0.000002013057,0.000651078,0.000008164082,0.001370669,0.000009011846,0.000319956,0.001251507],"study_design_scores_gemma":[0.001403016,0.001568621,0.9961931,0.00001248883,0.00001267092,0.0002046726,0.0002805303,0.000003405961,0.0002095648,0.00004468795,0.000006745543,0.00006053483],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9935413,0.005820788,0.00008088381,0.0003475156,0.00002982788,0.000129194,0.00000878496,9.171704e-7,0.00004080037],"genre_scores_gemma":[0.9981498,0.00163494,0.00006899972,0.00002701742,0.00008135851,3.993598e-7,0.000003606493,0.000008356213,0.00002558159],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.004608453,"threshold_uncertainty_score":0.1826376,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01174944430011098,"score_gpt":0.2883726571998351,"score_spread":0.2766232128997241,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}