{"id":"W2894515985","doi":"10.1016/j.nicl.2018.09.026","title":"Unique degeneration signatures in the cerebellar cortex for spinocerebellar ataxias 2, 3, and 7","year":2018,"lang":"en","type":"article","venue":"NeuroImage Clinical","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":47,"is_retracted":false,"has_abstract":true,"ca_institutions":"Western University","funders":"Canada First Research Excellence Fund; Consejo Nacional de Ciencia y Tecnología; James S. McDonnell Foundation","keywords":"Degeneration (medical); Cerebellar Degeneration; Spinocerebellar ataxia; Cerebellum; Neuroscience; Cerebellar cortex; Neurodegeneration; Ataxia; Pathology; Biology; Psychology; Medicine; Disease","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0006589395,0.0003552188,0.0005016288,0.00244454,0.0003190342,0.0006566766,0.0001999944,0.0003508332,0.0006380864],"category_scores_gemma":[0.001501907,0.0001991556,0.0003915489,0.0006340505,0.0004148273,0.0002923963,0.0005137463,0.0001783912,0.0002250974],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003437123,"about_ca_system_score_gemma":0.0003517601,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.004619945,"about_ca_topic_score_gemma":0.0128649,"domain_scores_codex":[0.9996513,0.00005692658,0.00004218274,0.0001150816,0.00008267246,0.00005177147],"domain_scores_gemma":[0.9993395,0.00009754043,0.000221479,0.0001189761,0.0001632931,0.00005911523],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001269919,0.0000927116,0.5339453,0.0002568298,0.0007045815,0.001375275,0.0007320699,0.001607627,0.4014241,0.0004378586,0.0005890667,0.05756463],"study_design_scores_gemma":[0.00002115533,0.0001900664,0.9668948,0.00002833949,0.000257508,0.003824861,0.0001955354,0.004278574,0.02333447,0.0003636876,0.0005871292,0.00002398611],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9962607,0.0005381431,0.002483349,0.00001372762,0.000003604679,0.0000170791,0.0002249581,0.00006092481,0.0003975247],"genre_scores_gemma":[0.9975182,0.0001382556,0.001801758,0.0000118452,0.000001903178,0.000008940307,0.0003584263,0.0000160747,0.0001446207],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.004619945,"threshold_uncertainty_score":0.009186149,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0922844438557797,"score_gpt":0.3804022725523408,"score_spread":0.2881178286965611,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}