{"id":"W2897968446","doi":"10.1007/8904_2018_136","title":"Acute and Chronic Management in an Atypical Case of Ethylmalonic Encephalopathy","year":2018,"lang":"en","type":"article","venue":"JIMD Reports","topic":"Sulfur Compounds in Biology","field":"Biochemistry, Genetics and Molecular Biology","cited_by":21,"is_retracted":false,"has_abstract":false,"ca_institutions":"Centre hospitalier de l'Université Laval; Centre Hospitalier Universitaire de Sherbrooke; Université de Sherbrooke; McGill University Health Centre","funders":"","keywords":"Decompensation; Thiosulfate; Medicine; Gastroenterology; Internal medicine; Discontinuation; Endocrinology; Anesthesia; Chemistry; Sulfur","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002146701,0.000104603,0.0001384233,0.00005288826,0.00003208747,0.000006240373,0.0000735892,0.0001392187,0.00002296204],"category_scores_gemma":[0.00001974981,0.00009652763,0.00003122568,0.00007010546,0.0002550888,0.000003509625,0.0001814702,0.00006165807,0.000001468939],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00002065538,"about_ca_system_score_gemma":0.00004208458,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00001309171,"about_ca_topic_score_gemma":0.0002846562,"domain_scores_codex":[0.9990148,0.00005162191,0.0002852913,0.0004013813,0.00005508949,0.0001918424],"domain_scores_gemma":[0.9993006,0.000005382583,0.0001102762,0.0004797368,0.00004841482,0.00005557985],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.0002778996,0.0002179453,0.130829,0.00006195276,0.0001594108,0.01961878,0.0002260073,0.000005304425,0.8213752,0.0002174077,0.0003788258,0.02663228],"study_design_scores_gemma":[0.00200727,0.005706278,0.1793382,0.00006490102,0.00017421,0.06877943,0.0002698872,0.0002883163,0.7163216,0.00186004,0.02430142,0.0008884016],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9980522,0.0005762259,0.0001329793,0.00002784159,0.0002447646,0.0001481452,0.000002158401,0.00000752237,0.0008081014],"genre_scores_gemma":[0.9980123,0.0001383509,0.001409194,0.00006520519,0.0001864541,0.00001725683,0.00002079062,0.00001098296,0.0001394766],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.1050535,"threshold_uncertainty_score":0.3936282,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01038014237555209,"score_gpt":0.2961180146686189,"score_spread":0.2857378722930668,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}