{"id":"W2898730441","doi":"10.1016/j.clim.2018.10.019","title":"Clinical presentation, immunologic features, and hematopoietic stem cell transplant outcomes for IKBKB immune deficiency","year":2018,"lang":"en","type":"article","venue":"Clinical Immunology","topic":"Immunodeficiency and Autoimmune Disorders","field":"Immunology and Microbiology","cited_by":30,"is_retracted":false,"has_abstract":false,"ca_institutions":"University of Saskatchewan; Royal University Hospital; Hospital for Sick Children; University of British Columbia; Children's Hospital of Winnipeg; University of Manitoba; SickKids Foundation; University of Toronto; BC Children's Hospital; CancerCare Manitoba","funders":"","keywords":"Hypogammaglobulinemia; Immune system; Primary immunodeficiency; Hematopoietic stem cell transplantation; Medicine; Immunology; Immunopathology; Immunodeficiency; Severe combined immunodeficiency; Immunity; Biology; Transplantation; Internal medicine; Antibody; Gene; Genetics","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow","sts","research_integrity"],"consensus_categories":[],"category_scores_codex":[0.002262706,0.0006169247,0.001578961,0.0002649317,0.0009780459,0.00005804428,0.001096708,0.001517834,0.0003143995],"category_scores_gemma":[0.0003984675,0.0005054325,0.0007851549,0.0003609828,0.004876769,0.0002140217,0.0003358547,0.001302672,0.0007763517],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00003054895,"about_ca_system_score_gemma":0.0001941116,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00007471205,"about_ca_topic_score_gemma":0.000007938809,"domain_scores_codex":[0.9936014,0.001163964,0.002670646,0.001244424,0.0000853058,0.001234223],"domain_scores_gemma":[0.9947883,0.002952677,0.0007380008,0.001161526,0.0003254947,0.0000340331],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"observational","study_design_scores_codex":[0.01091118,0.0139592,0.2078086,0.0005403107,0.005761051,0.00006483441,0.0115292,0.000007448554,0.2079028,0.04387475,0.008665799,0.4889748],"study_design_scores_gemma":[0.02386088,0.00901452,0.8332188,0.0001755282,0.001034562,0.0005895064,0.005727369,0.00002842134,0.01950162,0.004073653,0.1007171,0.002057952],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.8814242,0.1063069,0.00130086,0.001054644,0.006765905,0.001206876,0.00008389582,0.000294671,0.001561956],"genre_scores_gemma":[0.988081,0.003733969,0.0001878165,0.0007029274,0.00004025835,0.0001503474,0.0001698361,0.00006243528,0.00687139],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.6254102,"threshold_uncertainty_score":0.9997784,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03235474263884226,"score_gpt":0.3326436047631264,"score_spread":0.3002888621242841,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}