{"id":"W2898730441","doi":"10.1016/j.clim.2018.10.019","title":"Clinical presentation, immunologic features, and hematopoietic stem cell transplant outcomes for IKBKB immune deficiency","year":2018,"lang":"en","type":"article","venue":"Clinical Immunology","topic":"Immunodeficiency and Autoimmune Disorders","field":"Immunology and Microbiology","cited_by":30,"is_retracted":false,"has_abstract":false,"ca_institutions":"University of Saskatchewan; Royal University Hospital; Hospital for Sick Children; University of British Columbia; Children's Hospital of Winnipeg; University of Manitoba; SickKids Foundation; University of Toronto; BC Children's Hospital; CancerCare Manitoba","funders":"","keywords":"Hypogammaglobulinemia; Immune system; Primary immunodeficiency; Hematopoietic stem cell transplantation; Medicine; Immunology; Immunopathology; Immunodeficiency; Severe combined immunodeficiency; Immunity; Biology; Transplantation; Internal medicine; Antibody; Gene; Genetics","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00028977,0.0004205482,0.0003629894,0.0008232547,0.000461592,0.000590193,0.000325012,0.0005040253,0.002769939],"category_scores_gemma":[0.001190276,0.0001524216,0.0003035615,0.0005808687,0.0004027886,0.000670974,0.0004026681,0.0004991409,0.0004051875],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003250848,"about_ca_system_score_gemma":0.0003135904,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0007703166,"about_ca_topic_score_gemma":0.0006552731,"domain_scores_codex":[0.999777,0.00003129766,0.00002932196,0.00003678037,0.0000308879,0.00009468468],"domain_scores_gemma":[0.9994573,0.0001335335,0.0001458597,0.0000200835,0.00003580465,0.0002073348],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0009863547,0.0001380302,0.9576309,0.00002921425,0.00002963649,0.03019416,0.0001393608,0.0001893216,0.003380645,0.0002201415,0.0006531237,0.006409167],"study_design_scores_gemma":[0.0000785753,0.0005544067,0.8486186,0.00007348959,0.00007670432,0.146648,0.0007945229,0.000741847,0.000877334,0.0006665849,0.0008461477,0.00002380394],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9956806,0.0006579122,0.0001243711,0.0001456947,0.00001156619,0.00001540112,0.00016898,0.00001194704,0.003183601],"genre_scores_gemma":[0.9992416,0.000184808,0.0000600861,0.00006339915,0.00002760485,0.000006345907,0.0002431787,0.000002647758,0.0001703389],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002769939,"threshold_uncertainty_score":0.009266376,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03235474263884226,"score_gpt":0.3326436047631264,"score_spread":0.3002888621242841,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}