{"id":"W2899277949","doi":"10.3390/cells7110188","title":"Neuronal Ceroid Lipofuscinoses: Connecting Calcium Signalling through Calmodulin","year":2018,"lang":"en","type":"article","venue":"Cells","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":11,"is_retracted":false,"has_abstract":true,"ca_institutions":"Trent University; University of Toronto; Dalhousie University","funders":"Natural Sciences and Engineering Research Council of Canada; Killam Trusts; Nova Scotia Health Research Foundation; Banting Research Foundation","keywords":"Batten disease; Calmodulin; Calcium signaling; Calcium-binding protein; Calcium; Biology; Cell biology; Signalling; Cathepsin D; Neuroscience; Biochemistry; Chemistry; Signal transduction; Enzyme; Gene","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001066376,0.0002686485,0.0002749672,0.000296918,0.0002525371,0.0004022227,0.000325273,0.0006241353,0.001071211],"category_scores_gemma":[0.0002231501,0.0001000581,0.000134444,0.0001904912,0.0005144944,0.000894793,0.0004692213,0.0005884677,0.0002029314],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004262253,"about_ca_system_score_gemma":0.0002681094,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001076084,"about_ca_topic_score_gemma":0.00145228,"domain_scores_codex":[0.9999198,0.00001553261,0.000006236875,0.00001527518,0.00001679453,0.00002635024],"domain_scores_gemma":[0.9999162,0.00002263268,0.00002723007,0.00000547618,0.00001179625,0.00001673206],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.0009763921,0.0000734713,0.007618409,0.0003404298,0.00002788188,0.005613531,0.0001889947,0.000259088,0.9686031,0.002952508,0.0003466392,0.0129996],"study_design_scores_gemma":[0.0002364226,0.0007322255,0.09454452,0.000120267,0.0001395015,0.02733373,0.0007411878,0.004577957,0.8392519,0.01165292,0.02061671,0.00005268161],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9537683,0.0337606,0.005551774,0.002280417,0.0001065122,0.00004590413,0.0001344739,0.00006333477,0.004288618],"genre_scores_gemma":[0.9898528,0.006588614,0.002011692,0.0002342522,0.00004910507,0.00001814422,0.00009405886,0.00000374143,0.001147524],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001076084,"threshold_uncertainty_score":0.00358355,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.05816445441093021,"score_gpt":0.33462601529587,"score_spread":0.2764615608849398,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}