{"id":"W2908689778","doi":"10.1097/mol.0000000000000578","title":"Chylomicron retention disease: genetics, biochemistry, and clinical spectrum","year":2019,"lang":"en","type":"review","venue":"Current Opinion in Lipidology","topic":"Pancreatitis Pathology and Treatment","field":"Medicine","cited_by":54,"is_retracted":false,"has_abstract":true,"ca_institutions":"Université de Montréal; Centre Hospitalier Universitaire Sainte-Justine","funders":"Canadian Institutes of Health Research","keywords":"Chylomicron; Hypocholesterolemia; Apolipoprotein B; COPII; Golgi apparatus; Biology; Endoplasmic reticulum; Microsomal triglyceride transfer protein; Vesicular transport protein; Biochemistry; Cholesterol; Secretory pathway; Very low-density lipoprotein; Lipoprotein","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002710104,0.0008992639,0.001415148,0.001324042,0.0001241633,0.0007327935,0.000506913,0.0007789596,0.002337512],"category_scores_gemma":[0.0007407068,0.0001536608,0.0003182073,0.001113812,0.0002337446,0.0007882648,0.0004230804,0.0007034789,0.001162274],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002904481,"about_ca_system_score_gemma":0.0005673795,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0004178615,"about_ca_topic_score_gemma":0.0003514401,"domain_scores_codex":[0.9998786,0.00002131881,0.00003411272,0.00002313936,0.00002843057,0.00001430021],"domain_scores_gemma":[0.9997007,0.0001214429,0.00006466196,0.000006848379,0.00006315593,0.00004320473],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0003512592,0.00006237374,0.00329032,0.02830864,0.0003753,0.01028938,0.0001615754,0.0003828184,0.005221241,0.001792524,0.1132485,0.836516],"study_design_scores_gemma":[0.00006417037,0.0001925439,0.009225095,0.008095886,0.0007878355,0.09166782,0.0002305788,0.0001773206,0.001505763,0.00160067,0.886398,0.0000543552],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.001085708,0.9966595,0.0002132203,0.0005929867,0.000524272,0.000006063274,0.00007539814,0.00002265599,0.000820192],"genre_scores_gemma":[0.005665813,0.9907866,0.0003825099,0.0006634963,0.001608048,0.00001017337,0.0002521843,0.000009382889,0.0006217841],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.002337512,"threshold_uncertainty_score":0.007819772,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.1787792577101554,"score_gpt":0.4577302840912185,"score_spread":0.2789510263810632,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}