{"id":"W2921046987","doi":"10.1093/jcag/gwz006.186","title":"A187 ERYTHROPOIETIC PROTOPORPHYRIA: AN UNUSUAL PRESENTATION OF ADVANCED LIVER FIBROSIS DURING INFANCY","year":2019,"lang":"en","type":"article","venue":"Journal of the Canadian Association of Gastroenterology","topic":"Porphyrin Metabolism and Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"BC Children's Hospital","funders":"","keywords":"Erythropoietic protoporphyria; Ferrochelatase; Medicine; Protoporphyrin; Liver biopsy; Cholestasis; Liver disease; Pathology; Gastroenterology; Internal medicine; Biopsy; Heme; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003124442,0.00008503184,0.0002219746,0.0001106429,0.00004235869,0.000006976777,0.0002415443,0.0001141517,0.00003384024],"category_scores_gemma":[0.000154598,0.00007276284,0.0001455128,0.00006928331,0.00004787828,0.00002116326,0.00003411395,0.0001113282,0.000001211116],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00006782339,"about_ca_system_score_gemma":0.0002133034,"about_ca_topic_candidate":true,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0009604544,"about_ca_topic_score_gemma":0.03085618,"domain_scores_codex":[0.9988949,0.0002120329,0.0003891289,0.0001025268,0.0001958447,0.0002055599],"domain_scores_gemma":[0.9983931,0.000009021355,0.001022147,0.0001808855,0.0002959163,0.00009892981],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0004056559,0.00004998619,0.857769,0.00003088223,0.0001050052,7.66538e-7,0.0001278818,0.0007732229,0.1401633,0.00002055247,0.0004534532,0.0001002948],"study_design_scores_gemma":[0.002187469,0.0009083991,0.9682536,0.00002386845,0.00005154486,0.00001849562,0.0001512815,0.0000156905,0.02741235,0.00005884564,0.0008624363,0.00005606739],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9987491,0.00005723105,0.00001703476,0.000459421,0.000349112,0.0002272888,0.00003138229,9.040351e-7,0.0001085667],"genre_scores_gemma":[0.9991749,0.00005128849,0.0002689209,0.0001452463,0.00008914133,0.000003408223,0.00001061587,0.000009533309,0.0002469259],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.1127509,"threshold_uncertainty_score":0.9868281,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.003342845665347599,"score_gpt":0.214991814579931,"score_spread":0.2116489689145834,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}