{"id":"W2944936314","doi":"10.46278/j.ncacn.20180622","title":"Applicability of Neuropsychological and Psychometric Tests in Autosomal Recessive Spastic Ataxia of Charlevoix-Saguenay (ARSACS)","year":2018,"lang":"en","type":"article","venue":"Neuropsychologie clinique et appliquée","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"Centre Intégré Universitaire de Santé et de Services Sociaux du Saguenay–Lac-Saint-Jean; Université de Sherbrooke; Université du Québec à Chicoutimi","funders":"","keywords":"Raven's Progressive Matrices; Dysarthria; Spinocerebellar ataxia; Neuropsychology; Population; Rating scale; Audiology; Psychology; Clinical psychology; Ataxia; Physical medicine and rehabilitation; Spastic; Medicine; Cognition; Psychiatry; Developmental psychology; Cerebral palsy","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":true,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001676213,0.0005195784,0.0003171618,0.001706639,0.0003171467,0.0004477693,0.0002457534,0.0003343446,0.0006804561],"category_scores_gemma":[0.005315966,0.00009715449,0.0003279674,0.0006472453,0.0005327851,0.0004324653,0.0006738497,0.0003197582,0.0002201313],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003186211,"about_ca_system_score_gemma":0.0002162074,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003065666,"about_ca_topic_score_gemma":0.00320007,"domain_scores_codex":[0.9993185,0.0002209094,0.0001395773,0.00007859014,0.0001429947,0.00009948832],"domain_scores_gemma":[0.998252,0.0005258722,0.0005492852,0.00007887699,0.0003673534,0.0002266024],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0002134078,0.00005726827,0.9854426,0.00002210269,0.00003580604,0.001267549,0.0007586495,0.000206462,0.0009661801,0.00002933506,0.00007444159,0.01092615],"study_design_scores_gemma":[0.000007463358,0.0004881633,0.9944989,0.00001518272,0.00002497092,0.003120335,0.0007144259,0.0002493904,0.0005455162,0.0000946432,0.0002320215,0.000009082295],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9991792,0.000210192,0.00005974752,0.00001292136,0.000002480647,0.000004559972,0.00003503179,0.000002571254,0.0004932669],"genre_scores_gemma":[0.9995562,0.0001124442,0.0001256961,0.000008348852,0.000002398716,0.000005161174,0.0000701079,9.082791e-7,0.0001186224],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003065666,"threshold_uncertainty_score":0.00886476,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0733972505066659,"score_gpt":0.3777695244935947,"score_spread":0.3043722739869288,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}